Abstract
Lymphangioma (LA) is a congenital benign malformation due to lymphatic vessel proliferation, resulting from the lack of communication between the venous system and the primitive lymphatic sacs. They are essentially enlarged lymph nodes with chylous or serous content covered by the endothelium. The most common localizations are the neck, followed by the axilla. Cystic lymphangiomas can be classified into two types: macrocystic, which is the most common, and microcystic, which is less frequent. In this article, we discuss the findings of a macrocystic lymphangioma of the right lateral chest wall in a five-year-old girl successfully treated in our department of pediatric surgery. The follow-up did not show any sign of recurrence after 12 months.