Abstract
Lung epithelioid hemangioendothelioma (LEHE) is a rare tumor of vascular origin with low to intermediate malignancy. Its diagnosis is confirmed by histopathology study. We report a case of a non-smoker man in his fifties who was diagnosed for LEHE with positive staining for erythroblast transformation-specific-related gene (ERG) and cluster of differentiation 31 (CD31). Our case highlights the importance of a histological diagnosis to avoid misdiagnosis.