Kaposiform Hemangioendothelioma with Kasabach-Merritt Phenomenon: A Rare Diagnosis of Neck Mass in a Child

Kaposiform hemangioendothelioma (KHE) is a rare aggressive vascular tumour of intermediate malignant potential and often associated with thrombocytopaenia, known as the Kasabach-Merritt phenomenon (KMP). Herein, we report a case of a 3-month-old child with a left neck mass, subsequently diagnosed with KHE, complicated with KMP. This case was managed with a multidisciplinary team involvement and successfully treated with the combination of steroids and sirolimus. As the diagnosis of KHE itself is rare, one may miss the differential diagnosis causing a delay in referral and subsequently late in diagnosis and initiating the treatment.