Abstract
We report the case of a 14-year-old boy who has been followed since four years ago for an extra-osseous cranial vault tumor, which has been removed due to its increase in size and its painful nature. The outcomes were marked by regression of the pain and the absence of recurrence. We described the clinical signs, MRI characteristics, surgery findings, and anatomopathological descriptions of this pediatric glomangioma and carried out a literature review about all the glomus tumors and cranial glomus tumors. It is the only case reported in the current literature on this topic.