Abstract
OBJECTIVE: To enhance the understanding of splenectomy in children with hereditary spherocytosis, specifically focusing on the preservation of accessory spleens or partial splenectomy. METHODS: A retrospective review of clinical data and surgical methods of a child with hereditary spherocytosis who underwent surgery for accessory spleen hyperfunction 7 years after splenectomy at the General Surgery Department of Anhui Provincial Children's Hospital, along with a literature review. RESULTS: The child successfully underwent single-port plus one laparoscopic accessory spleenectomy. The surgery lasted 195 min, with an estimated blood loss of 600 ml. The postoperative hospital stay was 8 days, and at 6 months of follow-up, there were no complications such as bleeding, wound infection, thrombosis, or adhesive intestinal obstruction. CONCLUSION: For children with hereditary spherocytosis, the decision to preserve the spleen or accessory spleens during surgical treatment offers important reference value.