Abstract
Proliferating pilar tumor (PPT) or proliferating trichilemmal tumor is a rare type of cutaneous tumors that predominantly affect the scalp of elderly women with an autosomal dominant pattern. However, no standardized management guidelines have been developed yet. In this article, we reported a rare incidence of the disease among Saudi Arabia's population with a literature review. A 40-year-old female patient presented with multiple and recurrent scalp swellings that were diagnosed as benign PPT and treated with repeated surgical excision.