Abstract
OBJECTIVES: Describe the clinical case of a RICH that was diagnosed in uterus, normally in obstetric ultrasounds they are often confused with arteriovenous malformations and other congenital tumors. The differential diagnosis of these entities is important, since they have a different evolution, prognosis and treatment. CLINICAL CASE: The clinical case of a RICH with incipient signs of heart failure is presented, it required an interdisciplinary approach with dermatologists, neonatologists, obstetricians and specialists in diagnostic imaging, to define diagnosis, conduct and follow-up. Postnatal follow-up was performed until complete and spontaneous involution, leaving almost no sequelae, despite the large size of the tumor. CONCLUSION: It is important to take into consideration the diagnosis of RICH, among intrauterine high-flow vascular tumors, so as not to perform unnecessary interventions.