Abstract
We report a case of a 32-year-old woman with gradually worsening dyspnea on exertion, where computed tomography (CT) angiography demonstrated a right-sided superior vena cava, which was seen dividing into two channels draining into the right atrium and left atrium, respectively. The present case highlights a rare anomaly, which can be considered to represent the extreme end of the spectrum of superior sinus venosus defect, as well as the role of CT angiography in identifying this rare surgically correctable cardiac defect that may cause cyanosis or a significant left-to-right shunt.