Abstract
Inflammatory myofibroblastic tumors are mesenchymal tumors typically found in the lung, abdominopelvic, and retroperitoneal regions, though they can occur throughout the body, with rare instances affecting the head and neck region. They present a diverse immunohistochemical profile, making diagnosis primarily reliant on such findings. Notably, fewer than fifty cases involving the head and neck, particularly the maxilla, have been reported in the literature, highlighting its rarity in this anatomical site. Herein, we report a case of IMT in the maxilla, managed through surgical excision and defect reconstruction using Patient-Specific Implants. Timely diagnosis is crucial to prevent potential morbidity, as undiagnosed cases may manifest as aggressive lesions. Thus, prompt intervention is imperative for optimal patient outcomes.