Gigantic lumbar aneurysmal bone cyst with abdominal extension in a pediatric patient: case report and its multidisciplinary management

儿童巨大腰椎动脉瘤样骨囊肿伴腹部延伸:病例报告及其多学科诊疗

阅读:1

Abstract

BACKGROUND: Aneurysmal bone cyst (ABC) is a rare, benign, and highly vascular osteolytic lesion characterized by expansile cystic spaces filled with blood and surrounded by thinned cortical bone. ABC is most commonly found in the vertebral column, most specifically in the posterior element of the lumbar spine. Management of spinal ABCs poses a challenge to the treating physician given its proximity to the neural structures. Surgical intervention, radiation therapy, cryotherapy, and embolization are effective treatment methods. However, no treatment protocol has been established in the literature, particularly when the tumor is uncommonly large. CASE DESCRIPTION: We present the case of a 12-year-old female with a flank mass and abdominal fullness, imaging showed a gigantic expansile lytic lesion with left sided extension to the visceral organs at the level of L4 with mild scoliotic deformity. A biopsy confirmed an ABC. Patient underwent embolization and sclerotherapy which failed to achieve tumor control. Patient was taken for anterior tumor intralesional excision with posterior instrumented fusion. Postoperatively patient symptoms, deformity and her overall alignment improved. CONCLUSIONS: The current case described the largest ABC spine tumor of the current pediatric literature. Multidisciplinary surgical management enabled satisfactory clinical and radiological outcomes with no recurrence at the last follow-up.

特别声明

1、本页面内容包含部分的内容是基于公开信息的合理引用;引用内容仅为补充信息,不代表本站立场。

2、若认为本页面引用内容涉及侵权,请及时与本站联系,我们将第一时间处理。

3、其他媒体/个人如需使用本页面原创内容,需注明“来源:[生知库]”并获得授权;使用引用内容的,需自行联系原作者获得许可。

4、投稿及合作请联系:info@biocloudy.com。