Abstract
A 37-year-old man who presented with upper abdominal pain was diagnosed with acute appendicitis. He underwent an open appendicectomy. The intraoperative findings included only an acutely inflamed appendix. Histopathological examination of the appendix showed an incidental finding of gastrointestinal stromal tumors (GISTs). This paper highlights the contributory factors that are assessed in the risk assessment of appendiceal GISTs. However, as these entities are rare, an accurate risk stratification and progression assessment tool has not been established yet.