Abstract
Unicystic ameloblastoma (UA) arising from a dentigerous cyst often leads to misinterpretation and undertreatment because of its higher recurrent potential, although it has a better prognosis than that of a solid or multicystic variant. This case is unique as UAs commonly develop in the posterior mandible and second decade of life. Here we report a case of 12-month-old infant with tumorous growth of the maxilla, making it difficult to diagnose because of varied clinical presentation. It also poses a treatment dilemma as the mural type of UA is notorious for recurring often requiring aggressive surgical resection or other adjuncts like chemical cauterization not routinely employed for dentigerous cysts. Conservative treatment further adds to the burden of misdiagnosis, thus requiring a longer follow-up period.