Abstract
Multiple dental anomalies are often associated with syndromes affecting the orofacial region. Macrodontia refers to the enlargement of a tooth and is relatively rarer than its counterpart, microdontia. Likewise, while the presence of multiple roots and root canals is common in permanent molars, a maxillary molar with a single root and a single root canal is extremely rare. Hyperdontia, or the presence of supernumerary teeth, most commonly occurs in the maxillary anterior and mandibular premolar regions. The occurrence of a maxillary distomolar is uncommon, and the development of a cyst around such a tooth is also rare. This case is reported for its rarity, as it involves multiple anomalies in a single non-syndromic individual, including macrodontia of the maxillary first molar with a single root and root canal, along with the presence of a distomolar on the same side of the maxillary arch.