Abstract
36-year-old lady with Primary Sjogren's Syndrome presented with progressive dyspnoea and dry cough since 6 months. On evaluation, there were multiple nodular cavitating lesions in lung on CT scan, which were hypermetabolic on FDG-PET. Biopsy was consistent with extra-nodal marginal zone B cell lymphoma of MALT. She was treated with Rituximab, Cyclophodphamide, Doxorubicin, Vincristine and Prednisolone based chemotherapy with good clinical and radiological response. Hence, lymphomas, including MALT lymphomas should be suspected when a Sjogren's patient presents with multiple pulmonary nodules.