Abstract
A male neonate was born at 40 weeks and 3 days gestation with bilateral, stellate shaped truncal lesions, consistent with type V aplasia cutis congenita (ACC). The infant was the survivor of a dichorionic diamniotic twin pregnancy, with fetal demise documented at 13 weeks gestation. Here we present a unique case of ACC associated with fetal papyraceus, along with a review of the current literature on this heterogeneous group of disorders.