Abstract
Papillon-Lefèvre syndrome (PLS) has a higher prevalence in the Kingdom of KSA (KSA) compared to many other parts of the world. Few case reports and case series have been reported from the KSA. The clinical characteristics of cases reported vary in severity and presentation. Variation in cases may involve differences in periodontal involvement and/or skin manifestation and other systemic involvement. Depending on the severity of periodontal involvement, treatment varies from oral hygiene instructions to implant placement for replacement of missing teeth in restoring esthetics. Studying the details of each case may help better manage PLS. An attempt was made to study all of the cases reported in the Saudi population to assess the clinical characteristics variation and treatment rendered. This compilation of cases could serve as a valuable resource and guiding source for dentists in KSA for the better management of patients diagnosed with PLS.