Abstract
Acute orbital compartment syndrome (AOCS) is a rare condition needing prompt surgical intervention to avoid irreversible visual loss. We present a two-year-old with decreased activity, head edema, pain, restricted ocular movement, proptosis, and downward displacement of the left eyeball after a minor fall. Upon thorough evaluation, hemophilia C was diagnosed. An MRI scan revealed a circumferential scalp hematoma and subperiosteal hematoma, causing proptosis of the left orbit. Surgical evacuation of the blood collection resulted in complete recovery and resolution of symptoms. In AOCS, bleeding diathesis must be ruled out, and prompt decompression treatment is recommended.