Abstract
Choledochal cysts are rare anatomical anomalies of the biliary tree. These lesions possess a risk for future development of catastrophic malignancy in the form of cholangiocarcinoma if left unaddressed, which is associated with a high mortality rate in cases of malignant transformation. The presenting symptoms of choledochal cysts are often nonspecific. The age of the initial onset of symptoms can vary, and some patients with choledochal cysts do not receive a diagnosis until reaching adulthood. Here, we present a case that serves as an example of early detection of this rare clinical finding for potentially devastating malignancy in a child who presented with nonspecific symptoms.