Abstract
Purpose: This study was aimed at presenting a case of Sturge-Weber syndrome and oculodermal melanocytosis in a pediatric patient and offering a viable treatment course to control the glaucoma in both eyes. Observations: A 5-year-old female presents with a large port-wine stain on the left side of her face, retinal pigment changes, and diffuse slate gray pigmentation of the sclera, consistent with Sturge-Weber syndrome and oculodermal melanocytosis. She underwent bilateral trabeculotomy, micropulse cyclophotocoagulation, and staged Ahmed tube insertion for the management of her glaucoma. The pressures have normalized bilaterally after tube insertion, with the last measurement of her eyes under anesthesia revealing intraocular pressures of 25 in the left and 18 in the right. Conclusions: It is possible to achieve intraocular pressure control in a patient with congenital glaucoma associated with Sturge-Weber syndrome and oculodermal melanocytosis using staged Ahmed tube insertion.