Abstract
Immunoglobulin G4-related disease is a rare systemic condition that can affect multiple organs, though involvement of the central nervous system is uncommon. This report discusses an unusual case of a 64-year-old man who experienced neurological symptoms due to a spinal lesion. Imaging revealed a compressive mass at the cervical spine level, which was surgically removed and later confirmed to be IgG4-related hypertrophic spinal pachymeningitis. This case highlights the importance of considering rare inflammatory conditions in the differential diagnosis of spinal lesions and emphasizes the role of histopathological confirmation for accurate diagnosis and treatment planning.