Abstract
Juvenile trabecular ossifying fibroma (JTOF) is a rare benign fibro-osseous tumor predominantly affecting the maxillofacial region in children and adolescents. This study represented a case of maxillary reconstruction using deep circumflex iliac artery (DCIA) flap for JTOF and systematically reviewed the clinical characteristics and management of JTOF. A systematic review of published studies was performed. Information including clinical features, management, and follow-up was collected. We reported a 15-year-old male with maxillary JTOF. The patient underwent maxillectomy followed by DCIA flap reconstruction guided by 3D-printed surgical guides. No recurrence during 24-month follow-up period. The systematic review included 43 articles and 86 cases. Tumors involved the maxilla and mandible equally, with an average diameter of 4.8 cm. The overall recurrence rate was 23.9%, with a mean follow-up period of 39.2 months. We systematically reviewed the clinical features of JTOF and reported a case managed with DCIA flap maxillary reconstruction. Larger cohorts and extended follow-up are needed to determine the optimal management strategy for this rare disease.