Hypocomplementemic Urticarial Vasculitis Syndrome: A Rare Form of Vasculitis

Hypocomplementemic urticarial vasculitis syndrome (HUVS) is a rare autoimmune disorder characterized by recurrent urticarial lesions and acquired hypocomplementemia with systemic manifestations. Systemic involvement can either be present at the onset of disease or develop later. Here, we present a rare case of a 22-year-old female, who initially presented with generalized rash and was eventually diagnosed with HUVS. She responded well to dapsone. This article emphasizes the importance of a comprehensive review of systemic manifestations accompanying urticaria.