Abstract
Hemangiopericytomas (HPCs) are rare vascular tumors originating from pericytes, with a predilection for the musculoskeletal system and occasional occurrence in the head and neck region. HPCs arising in the external auditory canal (EAC) are exceptionally rare, making their diagnosis and management a clinical challenge. A 71-year-old male presented with a six-month history of a painless, progressively enlarging mass in his right EAC, accompanied by tinnitus and hearing loss. Physical examination revealed a mobile, reddish mass in the concha of the left auricle, nearly occluding the EAC. Contrast-enhanced computed tomography of the temporal bone demonstrated a heterogeneously enhancing mass with erosion of adjacent structures. Histopathological examination and immunohistochemistry confirmed the diagnosis of an HPC. The tumor was surgically excised, and the patient underwent adjuvant radiotherapy. Over a two-year follow-up period, no recurrence was observed. This case highlights the rarity of HPCs in the EAC and underscores the importance of considering this diagnosis in patients presenting with atypical EAC masses. A multidisciplinary approach, including surgical excision and radiotherapy, is crucial for achieving favorable outcomes and reducing the risk of recurrence. Long-term follow-up is essential due to the potential for late recurrence.