Abstract
Absence of right superior vena cava with a persistent left superior vena cava is rare. We report a case of an 8-month-old child who presented with a ventricular septal defect, absent right superior vena cava, and a persistent left superior vena cava. This case report describes the potential problems during cardiac surgery in this anomaly and its clinical implications. SUPPLEMENTARY INFORMATION: The online version contains supplementary material available at 10.1007/s12055-025-02152-x.