Abstract
Epithelioid hemangioendothelioma (EHE) is a rare condition arising from endothelial cells of the blood vessels. This is a vascular tumor that may occur anywhere throughout the body. This tumor behaves on a spectrum as either a benign tumor or an aggressive sarcoma. The EHE tumor and its management depend on the location of the lesion and accessibility for surgical excision. This case is a rare example of a patient presenting with a maxillary aggressive EHE tumor. This lesion was incidentally found on head CT done for ruling out fractures of the mid-face with incidental findings of an asymptomatic destructive lytic lesion. The treatment of this tumor located in a vital region of the mid-face will be discussed.