Abstract
Neurofibroma may occur as a sporadic solitary lesion or as a part of neurofibromatosis,an autosomal dominant disorder first described by Daniel Friedrich von Recklinghausen in1882. Angioneurofibroma is considered as a new morphological variant of neurofibroma. These lesions can be mixed histopathologically with vascular tumors. A female patient presented with right side facial swelling,which is seen at childhood.On examination mass was measuring around 10 × 10 cm over right fronto temporoparietal region,which is soft in consistency and nodularity in between, pigmentary changes seen over overlying skin in some area, tumor is painless,not associated with functional deformity, not associated with thrill or fluctuancy,causing facial deformity. The mass was intially diagnosed as vascular malformation, however with subsequent histopathlogical assessment confirmed the diagnosis of Angioneurofibroma. We present our experience in managing this rare case.