Abstract
INTRODUCTION: Skin tumors are prevalent in the head and neck especially auricle but pilomatricoma is extremely rare in ear lobule. CASE REPORT: A 7-year-old girl without a history of previous illness presented with a 1.5-month history of a lesion in the right ear lobule that tended to grow in size. It was a 2*2*2cm round, slightly painful lesion with soft tissue and light red in color that yielded bloody or serous fluid on aspiration. The lesion was enucleated. The diagnosis was pilomatricoma. CONCLUSION: Although very rare, pilomatricoma should be considered as a differential diagnosis of ear lobule neoplasms.