Abstract
Congenital cystic adenomatoid malformation of the lung (CCAM) is a congenital lung defect characterized by the formation of cysts of varying sizes at different stages of lung morphogenesis. Due to shared causes of embryogenesis disorders, CCAM is associated with other congenital malformations (CMs) in 10-20% of cases. One such CM, an esophageal duplication cyst (EDC), originates from the foregut and accounts for 10-15% of all gastrointestinal tract duplications. The occurrence of CCAM and EDC together in children is rare, with only five documented cases identified in our research. In this report, we present a case of a 16-year-old boy in whom both CCAM and EDC were detected incidentally during a routine examination. Following further evaluation, the patient underwent simultaneous lobectomy and EDC excision using uniportal video-assisted thoracoscopic surgery (uVATS). This case report highlights that simultaneous surgery using uVATS is a safe and effective approach for the management of CMs in the pediatric population.