日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Antisense oligonucleotide-mediated knockdown therapy in two infants with severe KCNT1 epileptic encephalopathy

反义寡核苷酸介导的基因敲低疗法治疗两名患有严重KCNT1癫痫性脑病的婴儿

Nakayama, Tojo; El Achkar, Christelle M; Burbano, Lisseth E; Quraishi, Imran H; Wu, Jing; Li, Melody; Asami, Yutaro; Golinski, Sean R; Sherrill, Emma; Goodlett, Benjamin D; de Gusmao, Claudio M; Friedman, Danielle A; Lentucci, Claudia; Suslovitch, Victoria; Riccardi, Olivia; Faour, Kamli N W; Kuniholm, Ashley; Soucy Verran, Aubrie; Coffman, Siobhan; Ahtam, Banu; Zhao, Boxun; Chin, Diana H; DiDonato, Renata L; Hu, Chunguang A; Lopez, Edith; Hills, Sonia; Maljevic, Snezana; Tran, Helene; Bush, Lynn W; Grant, Patricia Ellen; Madsen, Joseph R; Smith, Richard S; Kaczmarek, Leonard K; Berde, Charles B; Yu, Timothy W

Blocking RAN translation without altering repeat RNAs rescues C9ORF72-related ALS and FTD phenotypes

阻断 RAN 翻译而不改变重复 RNA 可挽救 C9ORF72 相关 ALS 和 FTD 表型

Jiang, Xin; Schaeffer, Laure; Patni, Divya; Russo, Tommaso; Lee, Chao-Zong; Aguilar, Corey; Marques, Christine; Jansen-West, Karen; Hruska-Plochan, Marian; Ray-Soni, Ananya; Lim, Su Min; Held, Aaron; Yue, Mei; Castellanos Otero, Paula; Aryal, Sandeep; Beaussant, Hortense D A M; Basu, Himanish; Takakuwa, Hiro; Daughrity, Lillian M; Ramesh, Nandini; Da Costa, Paulo; A A Quadros, Ana Rita; Nolan, Matthew; Reyes, Charles Jourdan F; Wheeler, Hayden; Moran, Laura C; Griesman, Grant; Wymann, Benjamin; Trombetta, Bianca A; Lopez-De-Silanes, Emma Sofia; Canori, Michael; Krishnan, Gopinath; Vieira Souza Da Silva, Yasmim; Eriani, Gilbert; Albers, Mark W; Arnold, Steven E; Song, Yuyu; Jain, Ankur; Chiu, Isaac M; Zhang, Yong-Jie; Gao, Fen-Biao; Wainger, Brian J; Polymenidou, Magdalini; Petrucelli, Leonard; Martin, Franck; Lagier-Tourenne, Clotilde

Tree diversity is changing across tropical Andean and Amazonian forests in response to global change

受全球变化的影响,热带安第斯山脉和亚马逊森林的树木多样性正在发生变化。

Fadrique, B; Costa, F; Cuesta, F; Arellano, G; Cayuela, L; Baker, T R; Draper, F C; Esquivel-Muelbert, A; Ter Steege, H; Bauters, M; Aguirre-Gutiérrez, J; Aguirre-Mendoza, Z; Alexiades, M N; Alvarez-Davila, E; Arets, E; Ayala, E; Aymard, C G A; Baccaro, F; Báez, S; Baraloto, C; Barbosa, R I; Barbosa Camargo, P; Barlow, J; Barni, P E; Barroso, J; Benchimol, M; Bennett, A C; Berenguer, E; Blanc, L; Bonal, D; Bongers, F; Brienen, R; Brown, F; Bt Andrade, M; Burban, B; Burnham, R J; Camargo, J L; Carvalho, S P C; Castilho, C; Chave, J; Coelho de Souza, F; Comiskey, J; da Costa, L; de Lima, R B; de Oliveira, E A; de Oliveira, R L C; de Oliveira Perdiz, R; De Rutte, J; Del Aguila-Pasquel, J; Derroire, G; Di Fiore, A; Disney, M; Duque, A; Emilio, T; Farfan-Rios, W; Fauset, S; Fearnside, P M; Feeley, K J; Feldpausch, T R; Ferreira, J; Ferreira, L; Flores Llampazo, G R; Galbraith, D; García-Cabrera, K; García Criado, M; Gloor, E; Grandez-Rios, J M; Hérault, B; Homeier, J; Honorio Coronado, E N; Huamantupa-Chuquimaco, I; Huaraca Huasco, W; Huillca-Aedo, Y T; Idárraga, Á; Jadán-Maza, O; Kalamandeen, M; Killeen, T J; Laurance, S G W; Laurance, W F; Levesley, A; Lopez, W; Macía, M J; Magnusson, W E; Malhi, Y; Manzatto, A G; Marimon, B S; Marimon Junior, B H; Martínez-Villa, J A; Medeiros, M B; Melgaço, K; Melo, L; Metzker, T; Monteagudo, A; Morandi, P S; Myers, J A; Nascimento, H M; Nascimento, R; Neill, D; Nieto-Ariza, B; Palacios, W A; Palacios-Ramos, S; Pallqui-Camacho, N C; Pardo Molina, G; Peacock, J; Peña, M A; Pennington, R T; Peñuela, M C; Peres, C A; Pérez, Á J; Pickavance, G C; Pinto, E; Pipoly, J; Pitman, N; Prieto, A; Ramírez-Angulo, H; Reis, S M; Restrepo, Z; Reynel, C; Ribeiro, S; Rivas-Torres, G; Rojas, R; Rudas, A; Salinas, N; Salomão, R P; Santana, F; Schietti, J; Schwartz, G; Serrano, J; Silman, M; Silva, C; Silva, C A; Silva, R C; Silva, R S A; Silva-Espejo, J; Silveira, M; Simon, M F; Soto-Shareva, Y C; Souza, P F; Storck-Tonon, D; Stropp, J; Swamy, V; Tello, J S; Terborgh, J; Thomas, R; Torres-Lezama, A; Vale, J D; Valenzuela Gamarra, L; van der Heijden, G; van der Hout, P; van der Meer, P J; Vasquez Martinez, R; Vedovato, L; Verbeeck, H; Vieira, I; Vieira, S A; Vilanova, E; Vinceti, B; Vos, V A; Zagt, R; Zuidema, P A; Phillips, O L

Author Correction: Tree diversity is changing across tropical Andean and Amazonian forests in response to global change

作者更正:受全球变化的影响,热带安第斯山脉和亚马逊森林的树木多样性正在发生变化。

Fadrique, B; Costa, F; Cuesta, F; Arellano, G; Cayuela, L; Baker, T R; Draper, F C; Esquivel-Muelbert, A; Ter Steege, H; Bauters, M; Aguirre-Gutiérrez, J; Aguirre-Mendoza, Z; Alexiades, M N; Alvarez-Davila, E; Arets, E; Ayala, E; Aymard, C G A; Baccaro, F; Báez, S; Baraloto, C; Barbosa, R I; Barbosa Camargo, P; Barlow, J; Barni, P E; Barroso, J; Benchimol, M; Bennett, A C; Berenguer, E; Blanc, L; Bonal, D; Bongers, F; Brienen, R; Brown, F; Bt Andrade, M; Burban, B; Burnham, R J; Camargo, J L; Carvalho, S P C; Castilho, C; Chave, J; Coelho de Souza, F; Comiskey, J; da Costa, L; de Lima, R B; de Oliveira, E A; de Oliveira, R L C; de Oliveira Perdiz, R; De Rutte, J; Del Aguila-Pasquel, J; Derroire, G; Di Fiore, A; Disney, M; Duque, A; Emilio, T; Farfan-Rios, W; Fauset, S; Fearnside, P M; Feeley, K J; Feldpausch, T R; Ferreira, J; Ferreira, L; Flores Llampazo, G R; Galbraith, D; García-Cabrera, K; García Criado, M; Gloor, E; Grandez-Rios, J M; Hérault, B; Homeier, J; Honorio Coronado, E N; Huamantupa-Chuquimaco, I; Huaraca Huasco, W; Huillca-Aedo, Y T; Idárraga, Á; Jadán-Maza, O; Kalamandeen, M; Killeen, T J; Laurance, S G W; Laurance, W F; Levesley, A; Lopez, W; Macía, M J; Magnusson, W E; Malhi, Y; Manzatto, A G; Marimon, B S; Marimon Junior, B H; Martínez-Villa, J A; Medeiros, M B; Melgaço, K; Melo, L; Metzker, T; Monteagudo, A; Morandi, P S; Myers, J A; Nascimento, H M; Nascimento, R; Neill, D; Nieto-Ariza, B; Palacios, W A; Palacios-Ramos, S; Pallqui-Camacho, N C; Pardo Molina, G; Peacock, J; Peña, M A; Pennington, R T; Peñuela, M C; Peres, C A; Pérez, Á J; Pickavance, G C; Pinto, E; Pipoly, J; Pitman, N; Prieto, A; Ramírez-Angulo, H; Reis, S M; Restrepo, Z; Reynel, C; Ribeiro, S; Rivas-Torres, G; Rojas, R; Rudas, A; Salinas, N; Salomão, R P; Santana, F; Schietti, J; Schwartz, G; Serrano, J; Silman, M; Silva, C; Silva, C A; Silva, R C; Silva, R S A; Silva-Espejo, J; Silveira, M; Simon, M F; Soto-Shareva, Y C; Souza, P F; Storck-Tonon, D; Stropp, J; Swamy, V; Tello, J S; Terborgh, J; Thomas, R; Torres-Lezama, A; Vale, J D; Valenzuela Gamarra, L; van der Heijden, G; van der Hout, P; van der Meer, P J; Vasquez Martinez, R; Vedovato, L; Verbeeck, H; Vieira, I; Vieira, S A; Vilanova, E; Vinceti, B; Vos, V A; Zagt, R; Zuidema, P A; Phillips, O L

TRUE-MOGAD Score: A Novel Scoring System to Identify MOGAD Among Positive MOG-IgG Test Results

TRUE-MOGAD评分:一种用于识别MOG-IgG检测阳性结果中MOGAD的新型评分系统

Vilaseca, Andreu; Filippatou, Angeliki G; Said, Yana; Sechi, Elia; Syc-Mazurek, Stephanie B; Cacciaguerra, Laura; Guo, Kai; Vorasoot, Nisa; Niederschweiberer, Moritz; Thakolwiboon, Smathorn; Sagen, Jessica A; Lopez-Chiriboga, Sebastian A; Tillema, Jan-Mendelt; Chen, John J; Pittock, Sean J; Sotirchos, Elias S; Flanagan, Eoin P

Predictive Utility of ViroFind Detection of Blood and CSF Virome for Viral Presence in Human Brain Tissue

ViroFind检测血液和脑脊液病毒组对预测人脑组织中病毒存在的效用

Dang, Xin; Hanson, Barbara A; Lopez, Melissa; Miller, Janet; Jimenez, Millenia; Koralnik, Igor J

Quinazolinones as Bioisosteres of Naphthoquinones: A Path to Potent HsDHODH Inhibitors with Optimized Properties

喹唑啉酮作为萘醌的生物等排体:获得具有优化性能的高效HsDHODH抑制剂的途径

Godoi, Bruna F; Bueno, Jéssica D; Silva, Wemenes J L; da Purificação, Aline D; Leite, Pedro I P; Dos Santos, Thiago; Freitas, Murillo; Silva, Daniel G; Silva, Tais C; de Moraes, Josué; Freitas, Caroline S; Mattos, Mayara; Souza, Thiago M L; Martin, Bianca A; Lopez, Renata F V; Nonato, M Cristina; Andrade, Carolina H; Emery, Flavio S

Repellent activity against Aedes aegypti and metabolomic profiling of Myrica gale L. essential oils from Irish boglands

爱尔兰沼泽地杨梅精油对埃及伊蚊的驱避活性及代谢组学分析

Whyms, Sophie E; Nagar, Shipra; Luker, Hailey A; Lopez, April D; Pigott, Maria; Hodkinson, Trevor R; Sheridan, Helen; Hansen, Immo A; Walsh, John J

Aptamer-linked immobilized sorbent assay for detection of VP1 of foot and mouth disease virus serotype O

利用适体连接的固定化吸附剂检测口蹄疫病毒O型血清型VP1蛋白

Quintela, Irwin A; Lopez-Magaña, Raymondo; Hwang, Anya; Vasse, Tyler; Wu, Vivian C H

Clinical Characteristics and Outcomes of Bloodstream Infections Caused by Metallo-β-Lactamase-Producing Enterobacterales in Argentina: A Subanalysis of the EMBARCAR Prospective Multicenter Cohort Study

阿根廷产金属β-内酰胺酶肠杆菌科细菌引起的血流感染的临床特征和结局:EMBARCAR前瞻性多中心队列研究的亚组分析

Cordova, Ezequiel; Balbuena, Juan Pablo; Mykietiuk, Analia; Farina, Javier; Gañete, Marcelo; Scapellato, Pablo; Lespada, María Inés; Nannini, Esteban; Contreras, Rosa; Cunto, Eleonora; Barcelona, Laura; Pasteran, Fernando; Salgueira, Claudia; Hojman, Martín; Blanco, Miriam; Lopez Alegre, Horacio; Cox Fernandez, William E; Ezcurra, Cecilia; Godoy, Darío; Biglia, María A; Lopez Furst, María José; Mendez, Gustavo; Aguirre Rios, María F; Altclas, Javier; Sanchez, César; Stryjewski, Martin E