日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Neuronal STING activation in amyotrophic lateral sclerosis and frontotemporal dementia

肌萎缩侧索硬化症和额颞叶痴呆症中的神经元 STING 激活

Christine Marques, Aaron Held, Katherine Dorfman, Joon Sung, Catherine Song, Amey S Kavuturu, Corey Aguilar, Tommaso Russo, Derek H Oakley, Mark W Albers, Bradley T Hyman, Leonard Petrucelli, Clotilde Lagier-Tourenne, Brian J Wainger

Gasdermin-E mediates mitochondrial damage in axons and neurodegeneration

Gasdermin-E介导轴突中的线粒体损伤和神经退行性变

Dylan V Neel ,Himanish Basu ,Georgia Gunner ,Matthew D Bergstresser ,Richard M Giadone ,Haeji Chung ,Rui Miao ,Vicky Chou ,Eliza Brody ,Xin Jiang ,Edward Lee ,Michelle E Watts ,Christine Marques ,Aaron Held ,Brian Wainger ,Clotilde Lagier-Tourenne ,Yong-Jie Zhang ,Leonard Petrucelli ,Tracy L Young-Pearse ,Alice S Chen-Plotkin ,Lee L Rubin ,Judy Lieberman ,Isaac M Chiu

iPSC motor neurons, but not other derived cell types, capture gene expression changes in postmortem sporadic ALS motor neurons

iPSC 运动神经元(而非其他衍生细胞类型)可捕捉死后散发性 ALS 运动神经元中的基因表达变化

Aaron Held, Michelle Adler, Christine Marques, Charles Jourdan Reyes, Amey S Kavuturu, Ana R A A Quadros, I Sandra Ndayambaje, Erika Lara, Michael Ward, Clotilde Lagier-Tourenne, Brian J Wainger

Steady-state regulation of COPII-dependent secretory cargo sorting by inositol trisphosphate receptors, calcium, and penta EF hand proteins

肌醇三磷酸受体、钙和五EF手蛋白对COPII依赖性分泌货物分选的稳态调节

Aaron Held, Jacob Lapka, John Sargeant, Jennet Hojanazarova, Alaa Shaheen, Samuel Galindo, Corina Madreiter-Sokolowski, Roland Malli, Wolfgang F Graier, Jesse C Hay

A reference human induced pluripotent stem cell line for large-scale collaborative studies

用于大规模合作研究的参考人诱导多能干细胞系

Caroline B Pantazis ,Andrian Yang ,Erika Lara ,Justin A McDonough ,Cornelis Blauwendraat ,Lirong Peng ,Hideyuki Oguro ,Jitendra Kanaujiya ,Jizhong Zou ,David Sebesta ,Gretchen Pratt ,Erin Cross ,Jeffrey Blockwick ,Philip Buxton ,Lauren Kinner-Bibeau ,Constance Medura ,Christopher Tompkins ,Stephen Hughes ,Marianita Santiana ,Faraz Faghri ,Mike A Nalls ,Daniel Vitale ,Shannon Ballard ,Yue A Qi ,Daniel M Ramos ,Kailyn M Anderson ,Julia Stadler ,Priyanka Narayan ,Jason Papademetriou ,Luke Reilly ,Matthew P Nelson ,Sanya Aggarwal ,Leah U Rosen ,Peter Kirwan ,Venkat Pisupati ,Steven L Coon ,Sonja W Scholz ,Theresa Priebe ,Miriam Öttl ,Jian Dong ,Marieke Meijer ,Lara J M Janssen ,Vanessa S Lourenco ,Rik van der Kant ,Dennis Crusius ,Dominik Paquet ,Ana-Caroline Raulin ,Guojun Bu ,Aaron Held ,Brian J Wainger ,Rebecca M C Gabriele ,Jackie M Casey ,Selina Wray ,Dad Abu-Bonsrah ,Clare L Parish ,Melinda S Beccari ,Don W Cleveland ,Emmy Li ,Indigo V L Rose ,Martin Kampmann ,Carles Calatayud Aristoy ,Patrik Verstreken ,Laurin Heinrich ,Max Y Chen ,Birgitt Schüle ,Dan Dou ,Erika L F Holzbaur ,Maria Clara Zanellati ,Richa Basundra ,Mohanish Deshmukh ,Sarah Cohen ,Richa Khanna ,Malavika Raman ,Zachary S Nevin ,Madeline Matia ,Jonas Van Lent ,Vincent Timmerman ,Bruce R Conklin ,Katherine Johnson Chase ,Ke Zhang ,Salome Funes ,Daryl A Bosco ,Lena Erlebach ,Marc Welzer ,Deborah Kronenberg-Versteeg ,Guochang Lyu ,Ernest Arenas ,Elena Coccia ,Lily Sarrafha ,Tim Ahfeldt ,John C Marioni ,William C Skarnes ,Mark R Cookson ,Michael E Ward ,Florian T Merkle

Endothelial cells regulate astrocyte to neural progenitor cell trans-differentiation in a mouse model of stroke

中风小鼠模型中内皮细胞调节星形胶质细胞向神经祖细胞的转分化

Wenlu Li, Emiri T Mandeville, Violeta Durán-Laforet, Norito Fukuda, Zhanyang Yu, Yi Zheng, Aaron Held, Ji-Hyun Park, Takafumi Nakano, Masayoshi Tanaka, Jingfei Shi, Elga Esposito, Wanting Niu, Changhong Xing, Kazuhide Hayakawa, Ignacio Lizasoain, Klaus van Leyen, Xunming Ji, Brian J Wainger, Maria A

Human sensorimotor organoids derived from healthy and amyotrophic lateral sclerosis stem cells form neuromuscular junctions

来自健康和肌萎缩侧索硬化症干细胞的人类感觉运动类器官形成神经肌肉接头

João D Pereira, Daniel M DuBreuil, Anna-Claire Devlin, Aaron Held, Yechiam Sapir, Eugene Berezovski, James Hawrot, Katherine Dorfman, Vignesh Chander, Brian J Wainger

Circuit Dysfunction in SOD1-ALS Model First Detected in Sensory Feedback Prior to Motor Neuron Degeneration Is Alleviated by BMP Signaling

SOD1-ALS 模型中的电路功能障碍首先在运动神经元变性之前的感觉反馈中检测到,并通过 BMP 信号传导得到缓解

Aaron Held, Paxton Major, Asli Sahin, Robert A Reenan, Diane Lipscombe, Kristi A Wharton

Human SOD1 ALS Mutations in a Drosophila Knock-In Model Cause Severe Phenotypes and Reveal Dosage-Sensitive Gain- and Loss-of-Function Components

果蝇基因敲入模型中的人类 SOD1 ALS 突变导致严重的表型并揭示剂量敏感的功能获得和丧失成分

Aslı Şahin, Aaron Held, Kirsten Bredvik, Paxton Major, Toni-Marie Achilli, Abigail G Kerson, Kristi Wharton, Geoff Stilwell, Robert Reenan

Penta-EF-Hand Protein Peflin Is a Negative Regulator of ER-To-Golgi Transport

五肽-EF-手蛋白 Peflin 是内质网至高尔基体运输的负调节剂

Mariah Rayl, Mishana Truitt, Aaron Held, John Sargeant, Kevin Thorsen, Jesse C Hay