日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Q1291H-CFTR molecular dynamics simulations and ex vivo theratyping in nasal epithelial models and clinical response to elexacaftor/tezacaftor/ivacaftor in a Q1291H/F508del patient

Q1291H-CFTR 分子动力学模拟和鼻上皮模型中的体外治疗分型以及 Q1291H/F508del 患者对 elexacaftor/tezacaftor/ivacaftor 的临床反应

Katelin M Allan, Miro A Astore, Egi Kardia, Sharon L Wong, Laura K Fawcett, Jessica L Bell, Simone Visser, Po-Chia Chen, Renate Griffith, Adam Jaffe, Sheila Sivam, Orazio Vittorio, Serdar Kuyucak, Shafagh A Waters

Comparing Cytology Brushes for Optimal Human Nasal Epithelial Cell Collection: Implications for Airway Disease Diagnosis and Research

比较细胞学刷以获得最佳的人类鼻上皮细胞收集效果:对呼吸道疾病诊断和研究的意义

Laura K Fawcett, Nihan Turgutoglu, Katelin M Allan, Yvonne Belessis, John Widger, Adam Jaffe, Shafagh A Waters

Molecular and Functional Characteristics of Airway Epithelium under Chronic Hypoxia

慢性缺氧条件下气道上皮的分子和功能特征

Sharon L Wong, Egi Kardia, Abhishek Vijayan, Bala Umashankar, Elvis Pandzic, Ling Zhong, Adam Jaffe, Shafagh A Waters

Transplacental transfer of RSV antibody in Australian First Nations infants

澳大利亚原住民婴儿呼吸道合胞病毒抗体的胎盘转移

Nusrat Homaira, Michael Binks, Gregory Walker, Natasha Larter, Katrina Clark, Megan Campbell, Lisa McHugh, Nancy Briggs, Joyce Nyiro, Sacha Stelzer-Braid, Nan Hu, Kristine Macartney, Tom Snelling, Saad B Omer, William Rawlinson, Ross Andrews, Adam Jaffe

Molecular Dynamics and Theratyping in Airway and Gut Organoids Reveal R352Q-CFTR Conductance Defect

气道和肠道类器官中的分子动力学和治疗分型揭示了 R352Q-CFTR 传导缺陷

Sharon L Wong, Nikhil T Awatade, Miro A Astore, Katelin M Allan, Michael J Carnell, Iveta Slapetova, Po-Chia Chen, Jeffry Setiadi, Elvis Pandzic, Laura K Fawcett, John R Widger, Renee M Whan, Renate Griffith, Chee Y Ooi, Serdar Kuyucak, Adam Jaffe, Shafagh A Waters

S945L-CFTR molecular dynamics, functional characterization and tezacaftor/ivacaftor efficacy in vivo and in vitro in matched pediatric patient-derived cell models

S945L-CFTR 分子动力学、功能表征和 tezacaftor/ivacaftor 在匹配的儿科患者来源细胞模型中的体内和体外疗效

Katelin M Allan, Miro A Astore, Laura K Fawcett, Sharon L Wong, Po-Chia Chen, Renate Griffith, Adam Jaffe, Serdar Kuyucak, Shafagh A Waters

Mesenchymal Stem Cell exosome delivered Zinc Finger Protein activation of cystic fibrosis transmembrane conductance regulator

间充质干细胞外泌体传递锌指蛋白激活囊性纤维化跨膜传导调节器

Olga Villamizar, Shafagh A Waters, Tristan Scott, Nicole Grepo, Adam Jaffe, Kevin V Morris

Molecular dynamics and functional characterization of I37R-CFTR lasso mutation provide insights into channel gating activity

I37R-CFTR 套索突变的分子动力学和功能表征为通道门控活性提供了见解

Sharon L Wong, Nikhil T Awatade, Miro A Astore, Katelin M Allan, Michael J Carnell, Iveta Slapetova, Po-Chia Chen, Alexander Capraro, Laura K Fawcett, Renee M Whan, Renate Griffith, Chee Y Ooi, Serdar Kuyucak, Adam Jaffe, Shafagh A Waters

Proton channel blockers inhibit Duox activity independent of Hv1 effects

质子通道阻滞剂可抑制 Duox 活性,且与 Hv1 效应无关

Monica Valencia Gattas, Adam Jaffe, Juliana Barahona, Gregory E Conner

Novel Antioxidant Therapy with the Immediate Precursor to Glutathione, γ-Glutamylcysteine (GGC), Ameliorates LPS-Induced Cellular Stress in In Vitro 3D-Differentiated Airway Model from Primary Cystic Fibrosis Human Bronchial Cells

新型抗氧化疗法采用谷胱甘肽的直接前体 γ-谷氨酰半胱氨酸 (GGC),可改善原发性囊性纤维化人支气管细胞体外 3D 分化气道模型中 LPS 诱导的细胞应激

Chris K Hewson, Alexander Capraro, Sharon L Wong, Elvis Pandzic, Ling Zhong, Bentotage S M Fernando, Nikhil T Awatade, Gene Hart-Smith, Renee M Whan, Shane R Thomas, Adam Jaffe, Wallace J Bridge, Shafagh A Waters