日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Loss of ADAMTS9 disrupts ciliogenesis and collagen homeostasis resulting in Nephronophthisis-like polycystic kidneys

ADAMTS9 的缺失会破坏纤毛发生和胶原蛋白稳态,导致类似肾痨的多囊肾。

Fischer, Sydney; Robert, Karyn L; Ahmed, Manu; Kane, Griffin I; Kavanaugh, Matthew A; Wang, Wei; Tran, Pamela V; Atukorale, Prabhani U; Nandadasa, Sumeda

Cleavage of the Meckel-Gruber syndrome protein TMEM67 by ADAMTS9 uncouples Wnt signaling and ciliogenesis.

ADAMTS9 对 Meckel-Gruber 综合征蛋白 TMEM67 的切割可使 Wnt 信号传导与纤毛发生解耦联

Ahmed Manu, Fischer Sydney, Robert Karyn L, Lange Karen I, Stuck Michael W, Best Sunayna, Johnson Colin A, Pazour Gregory J, Blacque Oliver E, Nandadasa Sumeda

Two functional forms of the Meckel-Gruber syndrome protein TMEM67 generated by proteolytic cleavage by ADAMTS9 mediate Wnt signaling and ciliogenesis.

由 ADAMTS9 蛋白水解切割产生的 Meckel-Gruber 综合征蛋白 TMEM67 的两种功能形式介导 Wnt 信号传导和纤毛发生

Ahmed Manu, Fischer Sydney, Robert Karyn L, Lange Karen I, Stuck Michael W, Best Sunayna, Johnson Colin A, Pazour Gregory J, Blacque Oliver E, Nandadasa Sumeda

CEP164C regulates flagellum length in stable flagella

CEP164C 调控稳定鞭毛中的鞭毛长度

Atkins, Madison; Týč, Jiří; Shafiq, Shahaan; Ahmed, Manu; Bertiaux, Eloïse; De Castro Neto, Artur Leonel; Sunter, Jack; Bastin, Philippe; Dean, Samuel Dale; Vaughan, Sue