日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Stability and Reproducibility Underscore Utility of RT-QuIC for Diagnosis of Creutzfeldt-Jakob Disease

稳定性和可重复性凸显了 RT-QuIC 在诊断克雅氏病方面的实用性

Maria Cramm, Matthias Schmitz, André Karch, Eva Mitrova, Franziska Kuhn, Bjoern Schroeder, Alex Raeber, Daniela Varges, Yong-Sun Kim, Katsuya Satoh, Steven Collins, Inga Zerr

Characteristic CSF prion seeding efficiency in humans with prion diseases

患有朊病毒疾病的人的典型脑脊液朊病毒播种效率

Maria Cramm, Matthias Schmitz, André Karch, Saima Zafar, Daniela Varges, Eva Mitrova, Bjoern Schroeder, Alex Raeber, Franziska Kuhn, Inga Zerr

De novo prion aggregates trigger autophagy in skeletal muscle

从头朊病毒聚集体引发骨骼肌自噬

Shivanjali Joshi-Barr, Cyrus Bett, Wei-Chieh Chiang, Margarita Trejo, Hans H Goebel, Beata Sikorska, Pawel Liberski, Alex Raeber, Jonathan H Lin, Eliezer Masliah, Christina J Sigurdson

Spongiform encephalopathy in transgenic mice expressing a point mutation in the β2-α2 loop of the prion protein

表达朊病毒蛋白 β2-α2 环点突变的转基因小鼠的海绵状脑病

Christina J Sigurdson, Shivanjali Joshi-Barr, Cyrus Bett, Olivia Winson, Giuseppe Manco, Petra Schwarz, Thomas Rülicke, K Peter R Nilsson, Ilan Margalith, Alex Raeber, David Peretz, Simone Hornemann, Kurt Wüthrich, Adriano Aguzzi