Lack of CFTR in skeletal muscle predisposes to muscle wasting and diaphragm muscle pump failure in cystic fibrosis mice
骨骼肌中 CFTR 的缺乏会导致囊性纤维化小鼠出现肌肉萎缩和膈肌泵衰竭
期刊:PLoS Genetics
影响因子:
doi:10.1371/journal.pgen.1000586
Maziar Divangahi, Haouaria Balghi, Gawiyou Danialou, Alain S Comtois, Alexandre Demoule, Sheila Ernest, Christina Haston, Renaud Robert, John W Hanrahan, Danuta Radzioch, Basil J Petrof