日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Multiomics dissection of human RAG deficiency reveals distinctive patterns of immune dysregulation but a common inflammatory signature.

对人类 RAG 缺陷的多组学分析揭示了独特的免疫失调模式,但具有共同的炎症特征。

Bosticardo Marita, Dobbs Kerry, Delmonte Ottavia M, Martins Andrew J, Pala Francesca, Kawai Tomoki, Kenney Heather, Magro Gloria, Rosen Lindsey B, Yamazaki Yasuhiro, Yu Hsin-Hui, Calzoni Enrica, Lee Yu Nee, Liu Can, Stoddard Jennifer, Niemela Julie, Fink Danielle, Castagnoli Riccardo, Ramba Meredith, Cheng Aristine, Riley Deanna, Oikonomou Vasileios, Shaw Elana, Belaid Brahim, Keles Sevgi, Al-Herz Waleed, Cancrini Caterina, Cifaldi Cristina, Baris Safa, Sharapova Svetlana, Schuetz Catharina, Gennery Andrew R, Freeman Alexandra F, Somech Raz, Choo Sharon, Giliani Silvia C, Güngör Tayfun, Drozdov Daniel, Meyts Isabelle, Moshous Despina, Neven Benedicte, Abraham Roshini S, El-Marsafy Aisha, Kanariou Maria, King Alejandra, Licciardi Francesco, Cruz-Muñoz Mario E, Palma Paolo, Poli Cecilia, Adeli Mehdi, Algeri Mattia, Alroqi Fayhan J, Bastard Paul, Bergerson Jenna R E, Booth Claire, Brett Ana, Burns Siobhan O, Butte Manish J, Padem Nurcicek, de la Morena M, Dbaibo Ghassan, de Ravin Suk See, Dimitrova Dimana, Djidjik Reda, Dorna Mayra B, Dutmer Cullen M, Elfeky Reem, Facchetti Fabio, Fuleihan Ramsay L, Geha Raif S, Gonzalez-Granado Luis I, Haljasmägi Liis, Ale Hanadys, Hayward Anthony, Hifanova Anna M, Ip Winnie, Kaplan Blanka, Kapoor Neena, Karakoc-Aydiner Elif, Kärner Jaanika, Keller Michael D, Dávila Saldaña Blachy J, Kiykim Ayça, Kuijpers Taco W, Kuznetsova Elena E, Latysheva Elena A, Leiding Jennifer W, Locatelli Franco, Alva-Lozada Guisela, McCusker Christine, Celmeli Fatih, Morsheimer Megan, Ozen Ahmet, Parvaneh Nima, Pasic Srdjan, Plebani Alessandro, Preece Kahn, Prockop Susan, Sakovich Inga S, Starkova Elena E, Torgerson Troy, Verbsky James, Walter Jolan E, Ward Brant, Wisner Elizabeth L, Draper Deborah, Myint-Hpu Katherine, Truong Pooi M, Lionakis Michail S, Similuk Morgan B, Walkiewicz Magdalena A, Klion Amy, Holland Steven M, Oguz Cihan, Bogunovic Dusan, Kisand Kai, Su Helen C, Tsang John S, Kuhns Douglas, Villa Anna, Rosenzweig Sergio D, Pittaluga Stefania, Notarangelo Luigi D

Impairment of Innate Immunity and Depletion of Vaccine-Induced Memory B and T Cells in the Absence of the Spleen

脾脏缺失导致先天免疫受损和疫苗诱导的记忆性B细胞和T细胞耗竭

Bordoni, Veronica; Cinicola, Bianca Laura; Piano Mortari, Eva; Castilletti, Concetta; Guarracino, Federica; Albano, Christian; Accordini, Silvia; Baban, Anwar; Di Sabatino, Antonio; Rossi, Carlo Maria; Lenti, Marco Vincenzo; Zicari, Anna Maria; Cirelli, Riccardo; Spada, Marco; Forni, Gian Luca; Quinti, Isabella; Algeri, Mattia; Casale, Maddalena; Perrotta, Silverio; Locatelli, Franco; Agrati, Chiara; Carsetti, Rita

Truncated form of human CD19 antigen as a suicide gene to control T-cell alloreactivity: ΔCD19

人类CD19抗原的截短形式作为一种自杀基因,用于控制T细胞同种异体反应性:ΔCD19

Manni, Simona; Iaffaldano, Laura; Guercio, Marika; Merli, Pietro; Del Bufalo, Francesca; Becilli, Marco; Algeri, Mattia; Pagliara, Daria; De Vito, Rita; Zugmaier, Gerhard; De Angelis, Biagio; Quintarelli, Concetta; Locatelli, Franco

Outcomes of children and young adults with B-cell acute lymphoblastic leukemia given blinatumomab as last consolidation treatment before allogeneic hematopoietic stem cell transplantation

接受blinatumomab作为异基因造血干细胞移植前最后一次巩固治疗的B细胞急性淋巴细胞白血病患儿和青少年的预后

Algeri, Mattia; Massa, Michele; Pagliara, Daria; Bertaina, Valentina; Galaverna, Federica; Pili, Ilaria; Li Pira, Giuseppina; Carta, Roberto; Quagliarella, Francesco; Pinto, Rita M; Rosignoli, Chiara; Lucarelli, Barbarella; Cefalo, Maria G; Boccieri, Emilia; Benini, Francesca; Del Bufalo, Francesca; Becilli, Marco; Merli, Pietro; Zugmaier, Gerhard; Locatelli, Franco

Extended clinical phenotypes and treatment modalities in 32 JAGN1-deficient patients: a multicenter study by ESID and EBMT IEWP

32例JAGN1缺陷患者的扩展临床表型和治疗方式:ESID和EBMT IEWP的多中心研究

Fekadu-Siebald, Julia; Salzmann-Manrique, Emilia; Heusel, Jan Robert; Willasch, Andre; Hauck, Fabian; Gonzalez-Granado, Luis Ignacio; Chavoshzadeh, Zahra; Sharafian, Samin; Cuntz, Franziska; Baris, Safa; Finocchi, Andrea; Algeri, Mattia; Sherkat, Roya; Klaudel-Dreszler, Maja; Zeidler, Cornelia; Bellanné-Chantelot, Christine; Kindle, Gerhard; Beaupain, Blandine; Paillard, Catherine; Seidel, Markus; Bader, Peter; Albert, Michael H; Neven, Bénédicte; Donadieu, Jean; Bakhtiar, Shahrzad

Point-of-care fresh CAR T cells for pediatric or young adult BCP-ALL that is relapsed/refractory or in very-high-risk first relapse

即时新鲜CAR-T细胞治疗复发/难治性或极高危首次复发的儿童或青少年BCP-ALL

Del Bufalo, Francesca; Becilli, Marco; Rosignoli, Chiara; Merli, Pietro; Algeri, Mattia; Pagliara, Daria; Galaverna, Federica; Massa, Michele; Paganelli, Valeria; Cefalo, Maria Giuseppina; Hanssens, Linda; Bertaina, Valentina; Li Pira, Giuseppina; Leone, Giovanna; Sinibaldi, Matilde; Di Cecca, Stefano; Iaffaldano, Laura; Fustaino, Valentina; De Angelis, Biagio; Quintarelli, Concetta; Locatelli, Franco

Relationship between pulse wave velocity progression and baseline heart rate and its change over 3.7 years of follow-up in hypertensive patients

高血压患者脉搏波速度进展与基线心率及其在3.7年随访期间变化的关系

Maloberti, Alessandro; Tognola, Chiara; Fumagalli, Stefano; Garofani, Ilaria; Algeri, Michela; Shkodra, Atea; Bellomare, Marco; Campana, Marta; Busti, Andrea; Riccio, Alfonso; Facchetti, Rita; Grassi, Guido; Bombelli, Michele; Giannattasio, Cristina

Clinical/pathological features and survival outcomes of extra-pulmonary neuroendocrine carcinomas: A retrospective single-center series

肺外神经内分泌癌的临床/病理特征和生存结局:一项回顾性单中心研究

Benini, L; Gervaso, L; Frassoni, S; Bagnardi, V; Cella, C A; Algeri, L; Ciardiello, D; Zampino, M G; Winchler, C; Boselli, S; Tamayo, D; Spada, F; Fazio, N

Outcomes of children with haematological malignancies given second haploidentical haematopoietic stem cell transplantation with either TCRαβ/CD19 depletion or post-transplant cyclophosphamide

接受第二次单倍体造血干细胞移植治疗血液系统恶性肿瘤患儿,并分别采用TCRαβ/CD19耗竭或移植后环磷酰胺治疗的疗效

Masetti, Riccardo; Leardini, Davide; Gottardi, Francesca; Baccelli, Francesco; Ottaviano, Giorgio Antonio Maria; Vendemini, Francesca; Saglio, Francesco; Pierri, Filomena; Algeri, Mattia; Del Bufalo, Francesca; Merli, Pietro; Prete, Arcangelo; Cesaro, Simone; Ussowicz, Marek; Faraci, Maura; Zecca, Marco; Fagioli, Franca; Balduzzi, Adriana; Dalle, Jean-Hugues; Locatelli, Franco; Pagliara, Daria

Exploring Barriers to Inclusivity: Systematic Analysis of Exclusion Criteria and Potential Bias in Clinical Cancer Trials for Psychiatric and Neurological Conditions in European Protocols

探索包容性的障碍:对欧洲方案中精神和神经系统疾病患者癌症临床试验的排除标准和潜在偏倚进行系统分析

Dahò, Margherita; Coppini, Veronica; Ferrari, Maria Vittoria; Ferraris, Giulia; Sanchini, Virginia; Monzani, Dario; Grasso, Roberto; Agnello, Chiara; Badalamenti, Giuseppe; Algeri, Laura; Pravettoni, Gabriella