日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

CD8 TRM-like T cells expressing perforin and IFN-γ define a pediatric activated T-cell acute liver failure endotype

表达穿孔素和IFN-γ的CD8 TRM样T细胞定义了儿童活化T细胞急性肝衰竭的内型

Diamond, Tamir; Chapin, Catherine A; Diorio, Caroline J; McCuaig, Sarah; Lau, Michelle; Chu, Niansheng; Gibson, Nora M; Kreiger, Portia A; Horslen, Simon; Loomes, Kathleen M; Banc-Husu, Anna M; Chu, Jaime; Jensen, M Kyle; Leung, Daniel H; Narang, Amrita; Carter, Beth A; Elisofon, Scott; Fischer, Ryan; Lobritto, Steven J; Leonis, Mike; Peters, Anna L; Rodriguez-Baez, Norberto; Romero, Rene; Rosenthal, Philip; Rudnick, David; Squires, James; Sundaram, Shikha; Tolliver, Kyla M; Valentino, Pamela; Durkalski, Valerie; Alonso, Estella M; Behrens, Edward M

Interleukin 8-CXCR2-mediated neutrophil extracellular trap formation in biliary atresia associated with neutrophil extracellular trap-induced stellate cell activation

胆道闭锁中白细胞介素 8-CXCR2 介导的中性粒细胞胞外陷阱形成与中性粒细胞胞外陷阱诱导的星状细胞活化相关

Luo, Yuhuan; Fraser, Lisa; Jezykowski, Julia; Gupta, Nitika A; Miethke, Alexander G; Taylor, Sarah A; Alonso, Estella M; Horslen, Simon; Kohli, Rohit; Molleston, Jean P; Kamath, Binita M; Guthery, Stephen L; Loomes, Kathleen M; Magee, John C; Rosenthal, Phillip; Valentino, Pamela; Sokol, Ronald J; Mack, Cara L

Defining a Histologic Scoring System for Gestational Alloimmune Liver Disease

妊娠期同种免疫性肝病组织学评分系统的定义

Conover, Katie R; Saul, Samantha; Chapin, Catherine A; Alonso, Estella M; Gupta, Anita; Bodmer, Jenna L; Lovell, Mark; Melin-Aldana, Hector; Taylor, Sarah A

Increased serum GM-CSF at diagnosis of biliary atresia is associated with improved biliary drainage.

胆道闭锁诊断时血清 GM-CSF 水平升高与胆道引流改善相关

Taylor Sarah A, Harpavat Sanjiv, Gromer Kyle D, Andreev Victor, Loomes Kathleen M, Bezerra Jorge A, Jarasvaraparn Chaowapong, Wang Kasper, Horslen Simon, Rosenthal Philip, Teckman Jeffrey, Valentino Pamela L, Ng Vicky L, Karpen Saul J, Sokol Ronald J, Alonso Estella M, Mack Cara L

Diagnostic accuracy of serum matrix metalloproteinase-7 as a biomarker of biliary atresia in a large North American cohort

血清基质金属蛋白酶-7作为胆道闭锁生物标志物的诊断准确性:一项北美大型队列研究

Pandurangi, Sindhu; Mourya, Reena; Nalluri, Shreya; Fei, Lin; Dong, Shun; Harpavat, Sanjiv; Guthery, Stephen L; Molleston, Jean P; Rosenthal, Philip; Sokol, Ronald J; Wang, Kasper S; Ng, Vicky; Alonso, Estella M; Hsu, Evelyn K; Karpen, Saul J; Loomes, Kathleen M; Magee, John C; Shneider, Benjamin L; Horslen, Simon P; Teckman, Jeffrey H; Bezerra, Jorge A

Protein biomarkers GDF15 and FGF21 to differentiate mitochondrial hepatopathies from other pediatric liver diseases

蛋白质生物标志物GDF15和FGF21可用于区分线粒体肝病与其他儿童肝病。

Van Hove, Johan L K; Friederich, Marisa W; Strode, Dana K; Van Hove, Roxanne A; Miller, Kristen R; Sharma, Rohit; Shah, Hardik; Estrella, Jane; Gabel, Linda; Horslen, Simon; Kohli, Rohit; Lovell, Mark A; Miethke, Alexander G; Molleston, Jean P; Romero, Rene; Squires, James E; Alonso, Estella M; Guthery, Stephen L; Kamath, Binita M; Loomes, Kathleen M; Rosenthal, Philip; Mysore, Krupa R; Cavallo, Laurel A; Valentino, Pamela L; Magee, John C; Sundaram, Shikha S; Sokol, Ronald J

Identification of pediatric activated T-cell hepatitis using clinical immune studies

利用临床免疫学研究鉴定儿童活化T细胞肝炎

Chapin, Catherine A; Diamond, Tamir; Perez, Adriana; Kreiger, Portia A; Loomes, Kathleen M; Behrens, Edward M; Alonso, Estella M

Serum bile acids as a prognostic biomarker in biliary atresia following Kasai portoenterostomy

血清胆汁酸作为葛西氏肝门空肠吻合术后胆道闭锁的预后生物标志物

Harpavat, Sanjiv; Hawthorne, Kieran; Setchell, Kenneth D R; Rivas, Monica Narvaez; Henn, Lisa; Beil, Charlotte A; Karpen, Saul J; Ng, Vicky L; Alonso, Estella M; Bezerra, Jorge A; Guthery, Stephen L; Horslen, Simon; Loomes, Kathy M; McKiernan, Patrick; Magee, John C; Merion, Robert M; Molleston, Jean P; Rosenthal, Philip; Thompson, Richard J; Wang, Kasper S; Sokol, Ronald J; Shneider, Benjamin L

Genotype-phenotype relationships of truncating mutations, p.E297G and p.D482G in bile salt export pump deficiency

胆汁酸输出泵缺陷中截断突变 p.E297G 和 p.D482G 的基因型-表型关系

Felzen, Antonia; van Wessel, Daan B E; Gonzales, Emmanuel; Thompson, Richard J; Jankowska, Irena; Shneider, Benjamin L; Sokal, Etienne; Grammatikopoulos, Tassos; Kadaristiana, Agustina; Jacquemin, Emmanuel; Spraul, Anne; Lipiński, Patryk; Czubkowski, Piotr; Rock, Nathalie; Shagrani, Mohammad; Broering, Dieter; Nicastro, Emanuele; Kelly, Deirdre; Nebbia, Gabriella; Arnell, Henrik; Fischler, Björn; Hulscher, Jan B F; Serranti, Daniele; Arikan, Cigdem; Polat, Esra; Debray, Dominique; Lacaille, Florence; Goncalves, Cristina; Hierro, Loreto; Muñoz Bartolo, Gema; Mozer-Glassberg, Yael; Azaz, Amer; Brecelj, Jernej; Dezsőfi, Antal; Calvo, Pier Luigi; Grabhorn, Enke; Hartleif, Steffen; van der Woerd, Wendy J; Kamath, Binita M; Wang, Jian-She; Li, Liting; Durmaz, Özlem; Kerkar, Nanda; Jørgensen, Marianne Hørby; Fischer, Ryan; Jimenez-Rivera, Carolina; Alam, Seema; Cananzi, Mara; Laverdure, Noemie; Ferreira, Cristina Targa; Guerrero, Felipe Ordoñez; Wang, Heng; Sency, Valerie; Kim, Kyung Mo; Chen, Huey-Ling; de Carvalho, Elisa; Fabre, Alexandre; Bernabeu, Jesus Quintero; Zellos, Aglaia; Alonso, Estella M; Sokol, Ronald J; Suchy, Frederick J; Loomes, Kathleen M; McKiernan, Patrick J; Rosenthal, Philip; Turmelle, Yumirle; Horslen, Simon; Schwarz, Kathleen; Bezerra, Jorge A; Wang, Kasper; Hansen, Bettina E; Verkade, Henkjan J

Heterogeneous liver on research ultrasound identifies children with cystic fibrosis at high risk of advanced liver disease

研究性超声检查发现肝脏异质性,可识别出患有囊性纤维化的儿童,这些儿童罹患晚期肝病的风险较高。

Siegel, Marilyn J; Leung, Daniel H; Molleston, Jean P; Ye, Wen; Paranjape, Shruti M; Freeman, A Jay; Palermo, Joseph J; Stoll, Janis; Masand, Prakash; Karmazyn, Boaz; Harned, Roger; Ling, Simon C; Navarro, Oscar M; Karnsakul, Wikrom; Alazraki, Adina; Schwarzenberg, Sarah Jane; Towbin, Alex J; Alonso, Estella M; Nicholas, Jennifer L; Green, Nicole; Otto, Randolph K; Magee, John C; Narkewicz, Michael R