Encephalopathy caused by ablation of very long acyl chain ceramide synthesis may be largely due to reduced galactosylceramide levels
极长酰基链神经酰胺合成受阻引起的脑病可能主要归因于半乳糖基神经酰胺水平降低。
期刊:Journal of Biological Chemistry
影响因子:3.9
doi:10.1074/jbc.M111.261206
Ben-David, Oshrit; Pewzner-Jung, Yael; Brenner, Ori; Laviad, Elad L; Kogot-Levin, Aviram; Weissberg, Itai; Biton, Inbal E; Pienik, Reut; Wang, Elaine; Kelly, Samuel; Alroy, Joseph; Raas-Rothschild, Annick; Friedman, Alon; Brügger, Britta; Merrill, Alfred H Jr; Futerman, Anthony H