日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

TDP-43 dysfunction leads to bioenergetic failure and lipid metabolic rewiring in human cells

TDP-43功能障碍会导致人类细胞生物能量衰竭和脂质代谢重编程。

Miriam Ceron-Codorniu ,Pascual Torres ,Anna Fernàndez-Bernal ,Santiago Rico-Rios ,José Ce Serrano ,Maria P Miralles ,Maria Beltran ,Ana Garcera ,Rosa M Soler ,Reinald Pamplona ,Manuel Portero-Otín

ERK MAPK signaling pathway inhibition as a potential target to prevent autophagy alterations in Spinal Muscular Atrophy motoneurons

ERK MAPK 信号通路抑制是预防脊髓性肌萎缩运动神经元自噬改变的潜在靶点

Alba Sansa, Maria P Miralles, Maria Beltran, Ferran Celma-Nos, Jordi Calderó, Ana Garcera #, Rosa M Soler #

Survival motor neuron protein and neurite degeneration are regulated by Gemin3 in spinal muscular atrophy motoneurons

在脊髓性肌萎缩症运动神经元中,存活运动神经元蛋白和神经突退化受 Gemin3 调控

Maria P Miralles, Alba Sansa, Maria Beltran, Rosa M Soler, Ana Garcera

Spinal Muscular Atrophy autophagy profile is tissue-dependent: differential regulation between muscle and motoneurons

脊髓性肌萎缩自噬特征是组织依赖性的:肌肉和运动神经元之间的差异调节

Alba Sansa, Ivan Hidalgo, Maria P Miralles, Sandra de la Fuente, M Jose Perez-Garcia, Francina Munell, Rosa M Soler #, Ana Garcera #

Intracellular pathways involved in cell survival are deregulated in mouse and human spinal muscular atrophy motoneurons

小鼠和人类脊髓性肌萎缩运动神经元中与细胞存活有关的细胞内通路失调

Alba Sansa, Sandra de la Fuente, Joan X Comella, Ana Garcera, Rosa M Soler

Calpain system is altered in survival motor neuron-reduced cells from in vitro and in vivo spinal muscular atrophy models

体外和体内脊髓性肌萎缩模型中存活的运动神经元减少细胞中的钙蛋白酶系统发生改变

Sandra de la Fuente, Alba Sansa, Iván Hidalgo, Nuria Vivancos, Ricardo Romero-Guevara, Ana Garcera #, Rosa M Soler #

Sp1-regulated expression of p11 contributes to motor neuron degeneration by membrane insertion of TASK1

Sp1 调节的 p11 表达通过 TASK1 的膜插入导致运动神经元变性

Victoria García-Morales, Guillermo Rodríguez-Bey, Laura Gómez-Pérez, Germán Domínguez-Vías, David González-Forero, Federico Portillo, Antonio Campos-Caro, Ángela Gento-Caro, Noura Issaoui, Rosa M Soler, Ana Garcera, Bernardo Moreno-López

Inhibition of autophagy delays motoneuron degeneration and extends lifespan in a mouse model of spinal muscular atrophy

抑制自噬可延缓脊髓性肌萎缩症小鼠模型中的运动神经元退化并延长寿命

Antonio Piras, Lorenzo Schiaffino, Marina Boido, Valeria Valsecchi, Michela Guglielmotto, Elena De Amicis, Julien Puyal, Ana Garcera, Elena Tamagno, Rosa M Soler, Alessandro Vercelli

Smn-Deficiency Increases the Intrinsic Excitability of Motoneurons

Smn 缺乏症会增加运动神经元的内在兴奋性

Saravanan Arumugam, Ana Garcera, Rosa M Soler, Lucía Tabares

The canonical nuclear factor-κB pathway regulates cell survival in a developmental model of spinal cord motoneurons

典型核因子-κB通路调节脊髓运动神经元发育模型中的细胞存活

Stefka Mincheva, Ana Garcera, Myriam Gou-Fabregas, Mario Encinas, Xavier Dolcet, Rosa M Soler