日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

High prevalence of treatable transthyretin cardiac amyloidosis in cardioembolic stroke: the first systematic cohort study

心源性栓塞性卒中患者中可治疗的转甲状腺素蛋白淀粉样变性患病率高:首个系统性队列研究

Harada, Shizuka; Nakajima, Makoto; Nomura, Toshiya; Kimura, Ryutaro; Matsubara, Soichiro; Misumi, Yohei; Kuyama, Naoto; Izumiya, Yasuhiro; Tsujita, Kenichi; Kimura, Kazumi; Ando, Yukio; Ueda, Mitsuharu

Genetic and clinical features of hereditary transthyretin amyloidosis: a decade of experience at a Japanese referral center

遗传性转甲状腺素蛋白淀粉样变性的遗传和临床特征:日本一家转诊中心十年的经验

Nomura, Toshiya; Misumi, Yohei; Tasaki, Masayoshi; Yamakawa, Shiori; Taguchi, Tomoaki; Obayashi, Konen; Yamashita, Taro; Ando, Yukio; Ueda, Mitsuharu

Dynamic changes of intracellular signals in ATTR Tyr114Cys amyloidosis

ATTR Tyr114Cys淀粉样变性中细胞内信号的动态变化

Ouchi, Kenta; Masuda, Takeshi; Yonemaru, Kou; Isono, Kaori; Ohya, Yuki; Shiraki, Nobuaki; Tasaki, Masayoshi; Inomata, Yukihiro; Ueda, Mitsuharu; Era, Takumi; Kume, Shoen; Ando, Yukio; Jono, Hirofumi

Real-World Utilization Patterns, Safety, and Efficacy of Tafamidis in Patients With Hereditary Transthyretin Amyloidosis in Japan

日本遗传性转甲状腺素蛋白淀粉样变性患者使用他法米地(Tafamidis)的真实世界应用模式、安全性和有效性

Konishi, Hiroaki; Abe, Hajime; Matsumoto, Noriko; Endo, Yutaka; Sekijima, Yoshiki; Ueda, Mitsuharu; Ando, Yukio

Senescence Accelerates the Occurrence of Dual Amyloidosis: Alzheimer's Disease and Wild-Type Transthyretin Amyloidosis

衰老加速双重淀粉样变性的发生:阿尔茨海默病和野生型转甲状腺素蛋白淀粉样变性

Misumi, Yohei; Ando, Yukio; Nakashima, Naoya; Sugimura, Yusuke; Shirahama, Ryo; Noguchi, Ryo; Matsuda, Hirofumi; Ando, Keiko; Tsunoda, Naoko; Izumiya, Yasuhiro; Tsujita, Kenichi; Ueda, Mitsuharu

Origin of Transthyretin in Cerebral Amyloid Angiopathy

脑淀粉样血管病中转甲状腺素蛋白的起源

Nomura, Toshiya; Misumi, Yohei; Tasaki, Masayoshi; Obayashi, Konen; Yamashita, Taro; Ando, Yukio; Ueda, Mitsuharu

Epidemiological study of the subtype frequency of systemic amyloidosis listed in the Annual of the Pathological Autopsy Cases in Japan

日本病理尸检病例年鉴中列出的系统性淀粉样变性亚型频率的流行病学研究

Yamaguchi, Aina; Tasaki, Masayoshi; Ueda, Mitsuharu; Ando, Yukio; Naiki, Hironobu

Eplontersen for Hereditary Transthyretin Amyloidosis With Polyneuropathy

Eplontersen 用于治疗伴有多发性神经病变的遗传性转甲状腺素蛋白淀粉样变性

Coelho, Teresa; Marques, Wilson Jr; Dasgupta, Noel R; Chao, Chi-Chao; Parman, Yesim; França, Marcondes Cavalcante Jr; Guo, Yuh-Cherng; Wixner, Jonas; Ro, Long-Sun; Calandra, Cristian R; Kowacs, Pedro A; Berk, John L; Obici, Laura; Barroso, Fabio A; Weiler, Markus; Conceição, Isabel; Jung, Shiangtung W; Buchele, Gustavo; Brambatti, Michela; Chen, Jersey; Hughes, Steven G; Schneider, Eugene; Viney, Nicholas J; Masri, Ahmad; Gertz, Morie R; Ando, Yukio; Gillmore, Julian D; Khella, Sami; Dyck, P James B; Waddington Cruz, Márcia

NSUN3-mediated mitochondrial tRNA 5-formylcytidine modification is essential for embryonic development and respiratory complexes in mice

NSUN3介导的线粒体tRNA 5-甲酰胞苷修饰对小鼠胚胎发育和呼吸链复合物至关重要。

Murakami, Yoshitaka; Wei, Fan-Yan; Kawamura, Yoshimi; Horiguchi, Haruki; Kadomatsu, Tsuyoshi; Miyata, Keishi; Miura, Kyoko; Oike, Yuichi; Ando, Yukio; Ueda, Mitsuharu; Tomizawa, Kazuhito; Chujo, Takeshi

Characteristics of Patients with Hereditary Transthyretin Amyloidosis-Polyneuropathy (ATTRv-PN) in NEURO-TTRansform, an Open-label Phase 3 Study of Eplontersen

NEURO-TTRansform(一项Eplontersen开放标签3期研究)中遗传性转甲状腺素淀粉样变性-多发性神经病(ATTRv-PN)患者的特征

Coelho, Teresa; Waddington Cruz, Márcia; Chao, Chi-Chao; Parman, Yeşim; Wixner, Jonas; Weiler, Markus; Barroso, Fabio A; Dasgupta, Noel R; Jung, Shiangtung W; Schneider, Eugene; Viney, Nicholas J; Dyck, P James B; Ando, Yukio; Gillmore, Julian D; Khella, Sami; Gertz, Morie A; Obici, Laura; Berk, John L