日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Overlapping forms of granulomatosis with polyangiitis and eosinophilic granulomatosis with polyangiitis: Insights from a European multicenter study

肉芽肿性多血管炎和嗜酸性肉芽肿性多血管炎的重叠类型:一项欧洲多中心研究的启示

Pallotti, Federica; Mettler, Camille; Papo, Matthias; Iudici, Michele; Padoan, Roberto; Sorin, Boris; Regola, Francesca; Franceschini, Franco; Moiseev, Sergey; Novikov, Pavel; Piga, Mario Andrea; Moroncini, Gianluca; Brix, Silke R; Kafagi, Abdul Hadi; Deshayes, Samuel; Aouba, Achille; Campagne, Julien; Delvino, Paolo; Tervaert, Jan Willem Cohen; Brussino, Luisa; Michaud, Martin; Venhoff, Nils; Alberici, Federico; Iannone, Claudia; Rosenstingl, Sophie; Moutel, Marin; Galempoix, Jean-Marc; Cottin, Vincent; Jaccard, Clara; Riehl, Diane; Legendre, Paul; Billet, Anne Claire; Parronchi, Paola; Quartuccio, Luca; Teixeira, Vitor; Egan, Allyson; Jayne, David; Tombetti, Enrico; Caminati, Marco; Pagnoux, Christian; Regent, Alexis; Ruivard, Marc; Guillevin, Loïc; Puéchal, Xavier; Terrier, Benjamin

Kidney Transplantation in Patients With Erdheim-Chester Disease

肾移植治疗埃尔德海姆-切斯特病

Palazzini, Giulia; Pegoraro, Francesco; Emile, Jean-François; Akkina, Sanjeev; Buti, Elisa; Perrone, Anna; Campochiaro, Corrado; Dagna, Lorenzo; La Porta, Edoardo; Chiarenza, Decimo Silvio; Peired, Anna J; Aouba, Achille; Renard-Penna, Raphaële; Haroche, Julien; Vaglio, Augusto

Complete PET/CT extinction and subsequent risk of aortic dilation in patients with giant cell arteritis-related large vessel vasculitis treated with tocilizumab

接受托珠单抗治疗的巨细胞动脉炎相关大血管炎患者出现PET/CT完全消退及随后发生主动脉扩张的风险

Dumont, Anaël; Espitia, Olivier; Samson, Maxime; Comarmond-Ortoli, Chloé; Sailler, Laurent; Berthoux, Emilie; Alexandra, Jean-François; Morard, Marie; Gallou, Sophie; Philip, Rémi; Martin-Silva, Nicolas; Maigné, Gwénola; Boutemy, Jonathan; Delacotte, Claire; Deshayes, Samuel; Aouba, Achille; de Boysson, Hubert

Functional changes in the gut microbiota are associated with the intestinal phenotype in A20 haploinsufficiency

肠道菌群的功能变化与A20单倍体不足的肠道表型相关

Elhani, Inès; Bredon, Marius; Enea, Diana; Desmons, Aurore; Arrive, Lionel; Bazille, Céline; Lefevre, Antoine; Aouba, Achille; Bigot, Adrien; de Moreuil, Claire; Alonso, Iria; Blasco, Hélène; Creusot, Laura; Dupuy, Camille; Emond, Patrick; Krasniqi, Pranvera; Lamaziere, Antonin; Oeuvray, Cyriane; Rainteau, Dominique; Svrcek, Magali; Rolhion, Nathalie; Sokol, Harry; Georgin-Lavialle, Sophie

Risk of Second Cancer in Erdheim-Chester Disease

Erdheim-Chester病患者罹患第二原发性癌症的风险

Pegoraro, Francesco; Peyronel, Francesco; Errahmani, Mohamed-Yassir; Catamerò, Francesco; Papo, Matthias; Cohen-Aubart, Fleur; Tesi, Michelangelo; Razanamahery, Jerome; Charlotte, Frederic; Le Scornet, Tanguy; Aouba, Achille; Roos-Weil, Damien; Tondo, Annalisa; Sieni, Elena; Amoura, Zahir; Emile, Jean-François; Annesi-Maisano, Isabella; Vaglio, Augusto; Haroche, Julien

Concordance between presenting features and relapse in granulomatosis with polyangiitis: implications for risk assessment and counselling

肉芽肿性多血管炎的临床表现与复发的一致性:对风险评估和咨询的启示

Iudici, Michele; Salis, Zubeyir; Cohen, Pascal; Néel, Antoine; Aouba, Achille; Lifermann, Francois; Ruivard, Marc; Aumaître, Olivier; Bonnotte, Bernard; Samson, Maxime; Maurier, Francois; Le Gallou, Thomas; Hachulla, Eric; Karras, Alexandre; Cottin, Vincent; Jourde-Chiche, Noemie; Viallard, Jean-François; Perier, Amandine; Godmer, Pascal; Quéméneur, Thomas; de Moreuil, Claire; Guillevin, Loïc; Terrier, Benjamin; Puéchal, Xavier

Prevalence estimation of a rare disease with the French National Rare Disease Registry: example of TNF receptor associated periodic syndrome (TRAPS)

利用法国国家罕见病登记处进行罕见病患病率估计:以TNF受体相关周期性综合征(TRAPS)为例

Subervie, Adrien; Elhani, Inès; Labouret, Mathilde; Georgin-Lavialle, Sophie; Hachulla, Eric; Belot, Alexandre; Hot, Arnaud; Quartier, Pierre; Aouba, Achille; Desdoits, Alexandra; Saadoun, David; Truchetet, Marie-Elise; Pillet, Pascal; Boursier, Guilaine; Benhamou, Ygal; Grall-Lerosey, Martine; Granel, Brigitte; Fain, Olivier; Queyrel, Viviane; Lescoat, Alain; Melki, Isabelle; Hentgen, Veronique

Vasodilator drugs and heart-related outcomes in systemic sclerosis: an exploratory analysis

血管扩张药物与系统性硬化症患者心脏相关结局:一项探索性分析

Guédon, Alexis F; Carrat, Fabrice; Mouthon, Luc; Launay, David; Chaigne, Benjamin; Pugnet, Grégory; Lega, Jean-Christophe; Hot, Arnaud; Cottin, Vincent; Agard, Christian; Allanore, Yannick; Fauchais, Anne Laure; Lescoat, Alain; Dhote, Robin; Papo, Thomas; Chatelus, Emmanuel; Bonnotte, Bernard; Kahn, Jean-Emmanuel; Diot, Elisabeth; Aouba, Achille; Magy-Bertrand, Nadine; Queyrel, Viviane; Le Quellec, Alain; Kieffer, Pierre; Amoura, Zahir; Granel, Brigitte; Gaultier, Jean Baptiste; Balquet, Marie-Hélène; Wahl, Denis; Lidove, Olivier; Espitia, Olivier; Cohen, Ariel; Fain, Olivier; Hachulla, Eric; Mekinian, Arsène; Rivière, Sébastien

A critical region of A20 unveiled by missense TNFAIP3 variations that lead to autoinflammation

TNFAIP3 错义变异揭示 A20 的关键区域,导致自身炎症

Elma El Khouri, Farah Diab, Camille Louvrier, Eman Assrawi, Aphrodite Daskalopoulou, Alexandre Nguyen, William Piterboth, Samuel Deshayes, Alexandra Desdoits, Bruno Copin, Florence Dastot Le Moal, Sonia Athina Karabina, Serge Amselem, Achille Aouba #, Irina Giurgea #

Intravenous versus subcutaneous tocilizumab in Takayasu arteritis: multicentre retrospective study

托珠单抗静脉注射与皮下注射治疗大动脉炎的多中心回顾性研究

Mekinian, Arsène; Biard, Lucie; Lorenzo, Dagna; Novikov, Pavel I; Salvarani, Carlo; Espitia, Olivier; Sciascia, Savino; Michaud, Martin; Lambert, Marc; Hernández-Rodríguez, José; Schleinitz, Nicolas; Awisat, Abid; Puechal, Xavier; Aouba, Achille; Munoz Pons, Helene; Smitienko, Ilya; Gaultier, Jean Baptiste; Edwige, Le Mouel; Benhamou, Ygal; Perlat, Antoinette; Jego, Patrick; Goulenok, Tiphaine; Sacre, Karim; Lioger, Bertrand; Hassold, Nolan; Broner, Jonathan; Dufrost, Virginie; Sené, Thomas; Seguier, Julie; Maurier, Francois; Berthier, Sabine; Belot, Alexandre; Frikha, Faten; Denis, Guillaume; Audemard-Verger, Alexandra; Koné-Paut, Isabelle; Humbert, Sebastien; Woaye-Hune, Pascal; Tomelleri, Alessandro; Baldissera, Elena Marina; Kuwana, Masataka; Lo Gullo, Alberto; Mukuchyan, Vahan; Dellal, Azeddine; Gaches, Francis; Zeminsky, Pierre; Galli, Elena; Alvarado, Moya; Boiardi, Luigi; Muratore, Francesco; Vautier, Mathieu; Campochiaro, Corrado; Moiseev, Sergey; Vieira, Matheus; Cacoub, Patrice; Fain, Olivier; Saadoun, David