N-glycan-mediated shielding of ADAMTS13 prevents binding of pathogenic autoantibodies in immune-mediated TTP
N-糖基化介导的ADAMTS13屏蔽作用可阻止致病性自身抗体在免疫介导的血栓性血小板减少性紫癜(TTP)中的结合。
期刊:Blood
影响因子:23.1
doi:10.1182/blood.2020007972
Ercig, Bogac; Graça, Nuno A G; Kangro, Kadri; Arfman, Tom; Wichapong, Kanin; Hrdinová, Johana; Kaijen, Paul; van Alphen, Floris P J; van den Biggelaar, Maartje; Vanhoorelbeke, Karen; Veyradier, Agnès; Coppo, Paul; Reutelingsperger, Chris; Nicolaes, Gerry A F; Männik, Andres; Voorberg, Jan