日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Stathmin-2 enhances motor axon regeneration after injury independent of its binding to tubulin

Stathmin-2 可促进损伤后运动轴突的再生,且该作用独立于其与微管蛋白的结合。

Beccari, Melinda S; Arnold-Garcia, Olatz; Baughn, Michael W; Artates, Jonathan W; McAlonis-Downes, Melissa; Lim, Jaisen; Leyva-Cázares, Dulce Fernanda; Rubio-Lara, Hugo Isaac; Ramirez-Rodriguez, Andrea; Bernal-Buenrostro, Carol N; Murgia-Bay, Brian; Rangel, Carolina K; Kim, Dong Hyun; Melamed, Ze'ev; Lutz, Cathleen M; Lagier-Tourenne, Clotilde; Corbett, Kevin D; López-Erauskin, Jone; Cleveland, Don W

Dual-targeting snRNA gene therapy rescues STMN2 and UNC13A splicing in TDP-43 proteinopathies

双靶向snRNA基因疗法可挽救TDP-43蛋白病中的STMN2和UNC13A剪接

Gomberg, Trent A; Elmsaouri, Sara; Kopalle, Hema M; Baughn, Michael W; Beccari, Melinda S; McAlonis-Downes, Melissa; Artates, Jonathan W; Pant, Deepak; Mak, Harriet; Smargon, Aaron A; Sander, Tynan C; Garcia, Esaul; Lee, Dominic P; Cleveland, Don W; Yeo, Gene W

Stathmin-2 loss leads to neurofilament-dependent axonal collapse driving motor and sensory denervation

Stathmin-2 的缺失会导致神经丝依赖性轴突塌陷,进而引发运动和感觉神经支配丧失。

López-Erauskin, Jone; Bravo-Hernandez, Mariana; Presa, Maximiliano; Baughn, Michael W; Melamed, Ze'ev; Beccari, Melinda S; Agra de Almeida Quadros, Ana Rita; Arnold-Garcia, Olatz; Zuberi, Aamir; Ling, Karen; Platoshyn, Oleksandr; Niño-Jara, Elkin; Ndayambaje, I Sandra; McAlonis-Downes, Melissa; Cabrera, Larissa; Artates, Jonathan W; Ryan, Jennifer; Hermann, Anita; Ravits, John; Bennett, C Frank; Jafar-Nejad, Paymaan; Rigo, Frank; Marsala, Martin; Lutz, Cathleen M; Cleveland, Don W; Lagier-Tourenne, Clotilde

Frontotemporal dementia-like disease progression elicited by seeded aggregation and spread of FUS

由 FUS 的种子聚集和扩散引起的额颞叶痴呆样疾病进展

Sonia Vazquez-Sanchez #, Britt Tilkin #, Fatima Gasset-Rosa #, Sitao Zhang, Diana Piol, Melissa McAlonis-Downes, Jonathan Artates, Noe Govea-Perez, Yana Verresen, Lin Guo, Don W Cleveland, James Shorter, Sandrine Da Cruz

Frontotemporal dementia-like disease progression elicited by seeded aggregation and spread of FUS

由FUS种子聚集和扩散引起的额颞叶痴呆样疾病进展

Vazquez-Sanchez, Sonia; Tilkin, Britt; Gasset-Rosa, Fatima; Zhang, Sitao; Piol, Diana; McAlonis-Downes, Melissa; Artates, Jonathan; Govea-Perez, Noe; Verresen, Yana; Guo, Lin; Cleveland, Don W; Shorter, James; Da Cruz, Sandrine

Mechanism of STMN2 cryptic splice-polyadenylation and its correction for TDP-43 proteinopathies

STMN2隐蔽剪接多聚腺苷酸化的机制及其对TDP-43蛋白病的纠正

Michael W Baughn,Ze'ev Melamed,Jone López-Erauskin,Melinda S Beccari,Karen Ling,Aamir Zuberi,Maximilliano Presa,Elena Gonzalo-Gil,Roy Maimon,Sonia Vazquez-Sanchez,Som Chaturvedi,Mariana Bravo-Hernández,Vanessa Taupin,Stephen Moore,Jonathan W Artates,Eitan Acks,I Sandra Ndayambaje,Ana R Agra de Almeida Quadros,Paayman Jafar-Nejad,Frank Rigo,C Frank Bennett,Cathleen Lutz,Clotilde Lagier-Tourenne,Don W Cleveland

Transient genomic instability drives tumorigenesis through accelerated clonal evolution

瞬时基因组不稳定性通过加速克隆进化推动肿瘤发生

Ofer Shoshani, Bjorn Bakker, Lauren de Haan, Andréa E Tijhuis, Yin Wang, Dong Hyun Kim, Marcus Maldonado, Matthew A Demarest, Jon Artates, Ouyang Zhengyu, Adam Mark, René Wardenaar, Roman Sasik, Diana C J Spierings, Benjamin Vitre, Kathleen Fisch, Floris Foijer, Don W Cleveland

Premature polyadenylation-mediated loss of stathmin-2 is a hallmark of TDP-43-dependent neurodegeneration

过早多聚腺苷酸化介导的 stathmin-2 丢失是 TDP-43 依赖性神经退行性疾病的标志

Ze'ev Melamed, Jone López-Erauskin, Michael W Baughn, Ouyang Zhang, Kevin Drenner, Ying Sun, Fernande Freyermuth, Moira A McMahon, Melinda S Beccari, Jon W Artates, Takuya Ohkubo, Maria Rodriguez, Nianwei Lin, Dongmei Wu, C Frank Bennett, Frank Rigo, Sandrine Da Cruz, John Ravits, Clotilde Lagier-To

Polyglutamine-Expanded Huntingtin Exacerbates Age-Related Disruption of Nuclear Integrity and Nucleocytoplasmic Transport

多聚谷氨酰胺扩增的亨廷顿蛋白加剧了与年龄相关的核完整性和核质运输破坏

Fatima Gasset-Rosa, Carlos Chillon-Marinas, Alexander Goginashvili, Ranjit Singh Atwal, Jonathan W Artates, Ricardos Tabet, Vanessa C Wheeler, Anne G Bang, Don W Cleveland, Clotilde Lagier-Tourenne

Exploring the effect of sequence length and composition on allele-selective inhibition of human huntingtin expression by single-stranded silencing RNAs.

探索序列长度和组成对单链沉默RNA选择性抑制人类亨廷顿蛋白表达的影响

Hu Jiaxin, Liu Jing, Yu Dongbo, Aiba Yuichiro, Lee Suheung, Pendergraff Hannah, Boubaker Jihane, Artates Jonathan W, Lagier-Tourenne Clotilde, Lima Walt F, Swayze Eric E, Prakash Thazha P, Corey David R