Dysregulation of TGF-beta1 receptor activation leads to abnormal lung development and emphysema-like phenotype in core fucose-deficient mice
TGF-β1受体激活失调会导致核心岩藻糖缺乏小鼠出现肺发育异常和类似肺气肿的表型。
期刊:Proceedings of the National Academy of Sciences of the United States of America
影响因子:9.1
doi:10.1073/pnas.0507375102
Wang, Xiangchun; Inoue, Shinya; Gu, Jianguo; Miyoshi, Eiji; Noda, Katsuhisa; Li, Wenzhe; Mizuno-Horikawa, Yoko; Nakano, Miyako; Asahi, Michio; Takahashi, Motoko; Uozumi, Naofumi; Ihara, Shinji; Lee, Seung Ho; Ikeda, Yoshitaka; Yamaguchi, Yukihiro; Aze, Yoshiya; Tomiyama, Yoshiaki; Fujii, Junichi; Suzuki, Keiichiro; Kondo, Akihiro; Shapiro, Steven D; Lopez-Otin, Carlos; Kuwaki, Tomoyuki; Okabe, Masaru; Honke, Koichi; Taniguchi, Naoyuki