日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Erdheim-Chester disease associated with myeloid neoplasm: Clinical features, molecular landscape, and treatment outcomes

Erdheim-Chester病合并髓系肿瘤:临床特征、分子图谱和治疗结果

Le Pogam, Ambroise; Papo, Matthias; Hirsch, Pierre; Cohen-Aubart, Fleur; Emile, Jean-François; Delhommeau, François; Duffau, Pierre; Razanamahery, Jérôme; Nguyen-Khac, Florence; Nunes Gomes, Christopher; Triboulet, Felicien; de La Rochefoucauld, Jeanne; McAvoy, Chloé; Lazaro, Estibaliz; Hage-Sleiman, Mehdi; Roos-Weil, Damien; Chasset, François; Jachiet, Vincent; Mekinian, Arsène; Fain, Olivier; Amoura, Zahir; Hadjadj, Jérôme; Haroche, Julien

Clinical Features and Biomarkers Associated With Intensive Care-Dependent Refractory NMDAR Encephalitis: A Retrospective Cohort Study

重症监护依赖型难治性NMDAR脑炎的临床特征和生物标志物:一项回顾性队列研究

Elosua-Bayes, Iker; Dumez, Pauline; Benaiteau, Marie; Ciano-Petersen, Nicolás Lundahl; Farina, Antonio; Villagrán-García, Macarena; Peter, Elise; Birzu, Cristina; Fourier, Anthony; Aubart, Mélodie; Picard, Geraldine; Do, Le Duy; Rogemond, Véronique; Goncalves, David; Psimaras, Dimitri; Honnorat, Jerome; Joubert, Bastien

Hyposplenism in systemic lupus erythematosus: biological and radiological characteristics and its association with increased risk of infection

系统性红斑狼疮合并脾功能减退:生物学和放射学特征及其与感染风险增加的关系

Trefond, Ludovic; Mathian, Alexis; Boussouar, Samia; Maloum, Karim; Settegrana, Catherine; Lhote, Raphael; Pha, Micheline; Papo, Matthias; Chasset, François; Cohen Aubart, Fleur; Haroche, Julien; Pereira, Bruno; Hie, Miguel; Amoura, Zahir

Severe thrombocytopenia in antiphospholipid syndrome: a retrospective study of 432 patients

抗磷脂综合征合并严重血小板减少症:一项对432例患者的回顾性研究

Schmidt, Carine; Papo, Matthias; Taïeb, Dov; Lhote, Raphaël; Hié, Miguel; Pha, Micheline; Haroche, Julien; Cohen-Aubart, Fleur; Cariou, Pierre-Louis; Ait Abdallah, Nassim; Mathian, Alexis; Moyon, Quentin; Amoura, Zahir

High risk of hypoxemic COVID-19 pneumonia in myasthenia gravis patients with type I IFN autoantibodies

重症肌无力患者若存在I型干扰素自身抗体,则发生低氧性COVID-19肺炎的风险较高

Gervais, Adrian; Marchal, Astrid; Maillard, Alexis; Le Voyer, Tom; Rosain, Jérémie; Philipot, Quentin; Bizien, Lucy; Peel, Jessica; Cederholm, Axel; Migaud, Mélanie; Pons, Sylvie; Saker, Kahina; Laforet, Pascal; Aubart, Mélodie; Gitiaux, Cyril; Biggs, Catherine; Leon Lopez, Rafael; Souvannanorath, Sarah; Tard, Céline; Nadaj Pakleza, Aleksandra; Grapperon, Aude-Marie; Heming, Nicholas; Annane, Djillali; Verschueren, Annie; Attarian, Shahram; Bigaut, Kévin; Hankiewicz, Karolina; Kouton, Ludivine; Villar-Quiles, Rocio-Nur; Cauquil, Cécile; Fleury, Marie-Céline; Rocher, Emilie; Nicolas, Guillaume; de Paula Estephan, Eduardo; da Penha Ananias Morita, Maria; Zanoteli, Edmar; Saied, Zakaria; Rachdi, Amine; Rim, Amouri; Belal, Samir; Ben Sassi, Samia; Hübers, Annemarie; Faure, Emmanuel; Desguerre, Isabelle; Basse, Clémence; Girard, Nicolas; Béziat, Vivien; Pan-Hammarström, Qiang; Hammarström, Lennart; Bodansky, Aaron; Parent, Audrey V; Anderson, Mark S; DeRisi, Joseph L; Demeret, Sophie; Truffault, Frédérique; Fort, Romain; Ader, Florence; Wallet, Florent; Abel, Laurent; Molina, Thierry; Alyanakian, Marie-Alexandra; Le Panse, Rozen; Solé, Guilhem; Cobat, Aurélie; Landegren, Nils; Casanova, Jean-Laurent; Puel, Anne; Bastard, Paul; Jouanguy, Emmanuelle

RAF-independent MEK mutations drive refractory histiocytic neoplasms but respond to ERK inhibition

RAF非依赖性MEK突变驱动难治性组织细胞肿瘤,但对ERK抑制剂有反应。

Eli L Diamond ,Jean-Francois Emile ,Takeshi Fujino ,Julien Haroche ,Maxim I Maron ,Alexander M Lewis ,Jahan Rahman ,Anne S Reiner ,Dana Bossert ,Marc Rosenblum ,Mariko Yabe ,Kseniya Petrova-Drus ,Jasmine H Francis ,Veronica Rotemberg ,Raajit K Rampal ,Sarah Yoo ,Anthony F Daniyan ,Sonia Mahajan ,Vaios Hatzoglou ,Robert Young ,Gary A Ulaner ,Wiebke Rösler ,Oshrat Hershkovitz-Rokah ,Ofer Shpilberg ,Roei D Mazor ,Luke Y C Chen ,Michael Singer ,M Adriana Cuibus ,Kenyon Weis ,Salima Benbarche ,Pu Zhang ,Nina Fox ,Cynthia Castro ,Steven Tittley ,Matthew Witkowski ,Fleur Cohen-Aubart ,Louis Terriou ,Maher Hanoun ,Nicolas Schleinitz ,Gabriela Sosa ,Timo Hautala ,Laure Farnault De Lassus ,Neal Rosen ,Omar Abdel-Wahab ,Benjamin H Durham

Risk of Second Cancer in Erdheim-Chester Disease

Erdheim-Chester病患者罹患第二原发性癌症的风险

Pegoraro, Francesco; Peyronel, Francesco; Errahmani, Mohamed-Yassir; Catamerò, Francesco; Papo, Matthias; Cohen-Aubart, Fleur; Tesi, Michelangelo; Razanamahery, Jerome; Charlotte, Frederic; Le Scornet, Tanguy; Aouba, Achille; Roos-Weil, Damien; Tondo, Annalisa; Sieni, Elena; Amoura, Zahir; Emile, Jean-François; Annesi-Maisano, Isabella; Vaglio, Augusto; Haroche, Julien

Role of clonal inflammatory microglia in histiocytosis-associated neurodegeneration

克隆性炎症小胶质细胞在组织细胞增生症相关神经退行性变中的作用

Rocio Vicario ,Stamatina Fragkogianni ,Maria Pokrovskii ,Carina Meyer ,Estibaliz Lopez-Rodrigo ,Yang Hu ,Masato Ogishi ,Araitz Alberdi ,Ann Baako ,Oyku Ay ,Isabelle Plu ,Véronique Sazdovitch ,Sebastien Heritier ,Fleur Cohen-Aubart ,Natalia Shor ,Makoto Miyara ,Florence Nguyen-Khac ,Agnes Viale ,Ahmed Idbaih ,Zahir Amoura ,Marc K Rosenblum ,Haochen Zhang ,Elias-Ramzey Karnoub ,Palash Sashittal ,Akhil Jakatdar ,Christine A Iacobuzio-Donahue ,Omar Abdel-Wahab ,Viviane Tabar ,Nicholas D Socci ,Olivier Elemento ,Eli L Diamond ,Bertrand Boisson ,Jean-Laurent Casanova ,Danielle Seilhean ,Julien Haroche ,Jean Donadieu ,Frederic Geissmann

MEK inhibitors are effective in Erdheim-Chester disease regardless of MAPK pathway mutations

无论MAPK通路是否存在突变,MEK抑制剂对Erdheim-Chester病均有效。

Pegoraro, Francesco; Cohen-Aubart, Fleur; Papo, Matthias; Catamerò, Francesco; Razanamahery, Jerome; Amoura, Zahir; Emile, Jean-François; Vaglio, Augusto; Haroche, Julien

Cluster analysis reveals the clinical spectrum of Erdheim-Chester disease

聚类分析揭示了埃尔德海姆-切斯特病的临床谱。

Tesi, Michelangelo; Pegoraro, Francesco; Peyronel, Francesco; Emile, Jean-François; Catamerò, Francesco; Koster, Matthew J; Goyal, Gaurav; Collin, Matthew; Milne, Paul; Boussouar, Samia; Cohen-Aubart, Fleur; Papo, Matthias; Amoura, Zahir; Estrada-Veras, Juvianee I; O'Brien, Kevin; Razanamahery, Jerome; Goulabchand, Radjiv; Idbaih, Ahmed; de Menthon, Mathilde; Gensous, Noemie; Aouba, Achille; Ledoult, Emmanuel; Le Scornet, Tanguy; Néel, Antoine; Go, Ronald S; Mazor, Roei D; Campochiaro, Corrado; Dagna, Lorenzo; Diamond, Eli L; Vaglio, Augusto; Haroche, Julien