日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

G3BP1-dependent mechanism suppressing protein aggregation in Huntington's models and its demise upon stress granule assembly

G3BP1 依赖机制抑制亨廷顿舞蹈症模型中的蛋白质聚集及其对应激颗粒组装的消亡

Ricardo Gutiérrez-Garcia, Seda Koyuncu, Franziska Hommen, Saygın Bilican, Hyun Ju Lee, Azra Fatima, David Vilchez

DNAJB6, a Key Factor in Neuronal Sensitivity to Amyloidogenesis

DNAJB6 是神经元对淀粉样变性敏感性的关键因素

Arun Thiruvalluvan, Eduardo P de Mattos, Jeanette F Brunsting, Rob Bakels, Despina Serlidaki, Lara Barazzuol, Paola Conforti, Azra Fatima, Seda Koyuncu, Elena Cattaneo, David Vilchez, Steven Bergink, Erik H W G Boddeke, Sjef Copray, Harm H Kampinga

The ubiquitin-conjugating enzyme UBE2K determines neurogenic potential through histone H3 in human embryonic stem cells

泛素结合酶 UBE2K 通过组蛋白 H3 决定人类胚胎干细胞中的神经发生潜力

Azra Fatima, Dilber Irmak, Alireza Noormohammadi, Markus M Rinschen, Aniruddha Das, Orsolya Leidecker, Christina Schindler, Víctor Sánchez-Gaya, Prerana Wagle, Wojciech Pokrzywa, Thorsten Hoppe, Alvaro Rada-Iglesias, David Vilchez

The ubiquitin ligase UBR5 suppresses proteostasis collapse in pluripotent stem cells from Huntington's disease patients

泛素连接酶 UBR5 抑制亨廷顿氏病患者多能干细胞的蛋白质稳态崩溃

Seda Koyuncu, Isabel Saez, Hyun Ju Lee, Ricardo Gutierrez-Garcia, Wojciech Pokrzywa, Azra Fatima, Thorsten Hoppe, David Vilchez

Mechanism suppressing H3K9 trimethylation in pluripotent stem cells and its demise by polyQ-expanded huntingtin mutations

抑制多能干细胞中 H3K9 三甲基化的机制及其由 polyQ 扩增的亨廷顿蛋白突变导致的消亡

Dilber Irmak, Azra Fatima, Ricardo Gutiérrez-Garcia, Markus M Rinschen, Prerana Wagle, Janine Altmüller, Laura Arrigoni, Barbara Hummel, Corinna Klein, Christian K Frese, Ritwick Sawarkar, Alvaro Rada-Iglesias, David Vilchez

Somatic increase of CCT8 mimics proteostasis of human pluripotent stem cells and extends C. elegans lifespan

CCT8 的体细胞增加模拟人类多能干细胞的蛋白质稳态并延长秀丽隐杆线虫的寿命

Alireza Noormohammadi, Amirabbas Khodakarami, Ricardo Gutierrez-Garcia, Hyun Ju Lee, Seda Koyuncu, Tim König, Christina Schindler, Isabel Saez, Azra Fatima, Christoph Dieterich, David Vilchez

Mesenchymal stem cells and their conditioned medium improve integration of purified induced pluripotent stem cell-derived cardiomyocyte clusters into myocardial tissue

间充质干细胞及其条件培养基可促进纯化的诱导多能干细胞衍生的心肌细胞簇整合到心肌组织中

Martin Rubach, Roland Adelmann, Moritz Haustein, Florian Drey, Kurt Pfannkuche, Bing Xiao, Annette Koester, Floris E A Udink ten Cate, Yeong-Hoon Choi, Klaus Neef, Azra Fatima, Tobias Hannes, Frank Pillekamp, Juergen Hescheler, Tomo Šarić, Konrad Brockmeier, Markus Khalil

The disease-specific phenotype in cardiomyocytes derived from induced pluripotent stem cells of two long QT syndrome type 3 patients

两例长 QT 综合征 3 型患者的诱导性多能干细胞来源的心肌细胞的疾病特异性表型

Azra Fatima, Shao Kaifeng, Sven Dittmann, Guoxing Xu, Manoj K Gupta, Matthias Linke, Ulrich Zechner, Filomain Nguemo, Hendrik Milting, Martin Farr, Jürgen Hescheler, Tomo Sarić

The novel desmin mutant p.A120D impairs filament formation, prevents intercalated disk localization, and causes sudden cardiac death

新型结蛋白突变体 p.A120D 会损害细丝形成,阻止闰盘定位,并导致心源性猝死

Andreas Brodehl, Mareike Dieding, Bärbel Klauke, Eric Dec, Shrestha Madaan, Taosheng Huang, John Gargus, Azra Fatima, Tomo Saric, Hamdin Cakar, Volker Walhorn, Katja Tönsing, Tim Skrzipczyk, Ramona Cebulla, Désirée Gerdes, Uwe Schulz, Jan Gummert, Jesper Hastrup Svendsen, Morten Salling Olesen, Dari

Dual color photoactivation localization microscopy of cardiomyopathy-associated desmin mutants

心肌病相关结蛋白突变体的双色光激活定位显微镜

Andreas Brodehl, Per Niklas Hedde, Mareike Dieding, Azra Fatima, Volker Walhorn, Susan Gayda, Tomo Šarić, Bärbel Klauke, Jan Gummert, Dario Anselmetti, Mike Heilemann, Gerd Ulrich Nienhaus, Hendrik Milting