Synthetic aminoglycosides efficiently suppress cystic fibrosis transmembrane conductance regulator nonsense mutations and are enhanced by ivacaftor
合成氨基糖苷类抗生素能有效抑制囊性纤维化跨膜传导调节因子无义突变,且其疗效可被伊伐卡托增强。
期刊:American Journal of Respiratory Cell and Molecular Biology
影响因子:5.3
doi:10.1165/rcmb.2013-0282OC
Xue, Xiaojiao; Mutyam, Venkateshwar; Tang, Liping; Biswas, Silpak; Du, Ming; Jackson, Laura A; Dai, Yanying; Belakhov, Valery; Shalev, Moran; Chen, Fuquan; Schacht, Jochen; J Bridges, Robert; Baasov, Timor; Hong, Jeong; Bedwell, David M; Rowe, Steven M