日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Somatic deficiency of the human E3 ubiquitin ligase CBL in leukocytes impairs B cell but not T cell development and function.

白细胞中人类 E3 泛素连接酶 CBL 的体细胞缺陷会损害 B 细胞的发育和功能,但不会影响 T 细胞的发育和功能。

Vatovec Taja, Neehus Anna-Lena, Jackson Katherine J L, Avery Danielle T, Bagarić Ivan, Erazo Lucia, Arango-Franco Carlos A, Ogishi Masato, Ahmed Syed F, Cederholm Axel, Russell Amanda J, Della Mina Erika, Al-Rifai Dena, Bull Rowena, Buetow Lori, Sobrino Steicy, Zhang Allison, Wahlster Lara, Michelet Marine, Parvaneh Nima, Peel Jessica, Barzaghi Federica, Leardini Davide, Philippot Quentin, Saettini Francesco, Dutrieux Jacques, de Muylder Benedicte, Vendemini Francesca, Baccelli Francesco, Catala Albert, Gambineri Eleonora, Veltroni Marinella, Pandiarajan Vignesh, Aguilar Yurena, Haerynck Filomeen, Elliott Michael, Turville Stuart, Brillot Fabienne, Khan Taushif, Consonni Filippo, Berteloot Laureline, Sewell William A, Rao Geetha, Largeaud Laetitia, Conti Francesca, Roullion Cecile, Masson Cécile, Pegoraro Francesco, Ye Tianyi, Joubran Samantha, Villalpando Emily, Bessot Boris, Seeleuthner Yoann, Le Voyer Tom, Rosain Jérémie, Li Hailun, Janda Zarah, Muratore Edoardo, Soudée Camille, Delabesse Eric, Goulvestre Claire, Shahrooei Mohammad, Puel Anne, André Isabelle, Bole-Feysot Christine, Abel Laurent, Erlacher Miriam, Béziat Vivien, Lagresle-Peyrou Chantal, Cheynier Remi, Six Emmanuelle, Marr Nico, Pasquet Marlène, Alsina Laia, Goodnow Christopher C, Landegren Nils, Aiuti Alessandro, Zhang Peng, Masetti Riccardo, Huang Danny T, Ma Cindy S, Casanova Jean-Laurent, Sankaran Vijay G, Bustamante Jacinta, Tangye Stuart G, Bohlen Jonathan

Neutropenia and infectious events during off-label treatment with venetoclax in children with malignant disease: a pharmacovigilance analysis of FDA adverse event reporting system reports

儿童恶性肿瘤患者接受维奈托克超适应症治疗期间发生中性粒细胞减少症和感染事件:基于FDA不良事件报告系统的药物警戒分析

Muratore, Edoardo; Giunchi, Valentina; Fusaroli, Michele; Baccelli, Francesco; Gottardi, Francesca; Poluzzi, Elisabetta; Masetti, Riccardo; Raschi, Emanuel

Prognostic value of cardiopulmonary exercise testing in pulmonary arterial hypertension

心肺运动试验对肺动脉高压的预后价值

Baccelli, Andrea; Rinaldo, Rocco F; Haji, Gulammehdi; Davies, Rachel J; Lo Giudice, Francesco; Gin-Sing, Wendy; Vigo, Beatrice; Centanni, Stefano; Gibbs, J Simon R; Howard, Luke S

Granulomatous lymphocytic interstitial lung disease in common variable immune deficiency: an in-depth clinical, immunological, functional and radiological exploration with a focus on its management, challenged by chronic CMV infection

常见变异型免疫缺陷患者的肉芽肿性淋巴细胞间质性肺病:深入的临床、免疫学、功能和放射学探讨,重点关注其治疗,以及慢性巨细胞病毒感染带来的挑战

Moratti, Mattia; Schifino, Gioacchino; Baccelli, Francesco; Ferrari, Simona; Magrini, Elisabetta; Bassi, Mirna; Guerrieri, Aldo; Zompatori, Maurizio; Lanari, Marcello; Conti, Francesca

The EASIX score as a predictor of sinusoidal obstruction syndrome and nonrelapse mortality in paediatric patients receiving allogeneic haematopoietic stem cell transplantation

EASIX评分作为接受异基因造血干细胞移植的儿科患者发生窦状隙阻塞综合征和非复发死亡率的预测指标

Muratore, Edoardo; Gambuti, Giacomo; Leardini, Davide; Baccelli, Francesco; Venturelli, Francesco; Larcinese, Leyna; Gottardi, Francesca; Di Battista, Antonia; Belotti, Tamara; Prete, Arcangelo; Masetti, Riccardo

Biallelic SH2B3 germline variants are associated with a neonatal myeloproliferative disease and multisystemic involvement

SH2B3基因双等位基因变异与新生儿骨髓增生性疾病和多系统受累相关。

Leardini, Davide; Flex, Elisabetta; Stieglitz, Elliot; Cerasi, Sara; Bertuccio, Salvatore Nicola; Baccelli, Francesco; Kállay, Krisztián; Kjollerstrom, Paula; Batalha, Sara; Carpentieri, Giovanna; Pedace, Lucia; Ciolfi, Andrea; Hammad, Mahmoud; Miranda, Maria; Rojas, Marta; Rao, Anupama; Innes, Andrew J; Rudelius, Martina; Santini, Valeria; Raddi, Marco; Teh, Kok-Hoi; De Vito, Rita; Yoshimi, Ayami; Tartaglia, Marco; Locatelli, Franco; Niemeyer, Charlotte M; Masetti, Riccardo

Phenotyping vasodilator responsiveness in idiopathic pulmonary arterial hypertension: any role for the cardiopulmonary exercise test?

特发性肺动脉高压血管舒张反应性的表型分析:心肺运动试验的作用是什么?

Sivasubramaniam, Gayathiri; Baccelli, Andrea; Haji, Gulam; Lo Giudice, Francesco; Weaver, Clare; Howard, Luke; Davies, Rachel

Clinical and prognostic role of tricuspid regurgitation in incident patients with pulmonary arterial hypertension

三尖瓣反流在肺动脉高压新发患者中的临床和预后作用

Ghio, Stefano; Moschella, Martina Marialaura; Baccelli, Andrea; Savonitto, Giulio; Maldera, Martina; Haji, Gulam; Davies, Rachel; Howard, Luke; Lo Giudice, Francesco

Real-Life Use of Posaconazole in Clinical Practice for Onco-Hematological Children: A National Survey by AIEOP Infectious Diseases Working Group

AIEOP传染病工作组开展的一项全国性调查:泊沙康唑在肿瘤血液病患儿临床实践中的实际应用

Chiusaroli, Lorenzo; Spadea, Manuela; Liberati, Cecilia; Petris, Maria Grazia; Grasso, Antonio; Baccelli, Francesco; Micheletti, Maria Vittoria; Gasperini, Pietro; D'Amico, Maria Rosaria; Perruccio, Katia; Barone, Angelica; Onofrillo, Daniela; Muggeo, Paola; Faraci, Maura; Rinieri, Simona; Liguoro, Ilaria; Colombini, Antonella; Trevisan, Francesca; Giurici, Nagua; Boscarol, Gianluca; Brescia, Letizia Pomponia; Pancaldi, Alessia; Compagno, Francesca; Biffi, Alessandra; Donà, Daniele; Cesaro, Simone

Unexplained breathlessness: Integrating pathophysiological insights with clinical evaluation

不明原因的呼吸困难:将病理生理学见解与临床评估相结合

Baccelli, Andrea; Giudice, Francesco Lo; Haji, Gulammehdi; Davies, Rachel J; Gin-Sing, Wendy; Howard, Luke S