R405W Desmin Knock-In Mice Highlight Alterations of Mitochondria, Protein Quality Control and Myofibrils in Myofibrillar Myopathy
R405W 结蛋白敲入小鼠揭示肌原纤维肌病中线粒体、蛋白质质量控制和肌原纤维的改变
期刊:Journal of Cachexia Sarcopenia and Muscle
影响因子:9.1
doi:10.1002/jcsm.70094
Batonnet-Pichon, Sabrina; Delort, Florence; Lilienbaum, Alain; Berwanger, Carolin; Schultheis, Dorothea; Schlötzer-Schrehardt, Ursula; Schmidt, Andreas; Uebe, Steffen; Baiche, Yosra; Eisenack, Tom J; Trentini, Débora Broch; Mallek, Markus; Mill, Leonid; Ferreiro, Ana; Eberhard, Bettina; Lücke, Thomas; Krüger, Markus; Thiel, Christian; Schröder, Rolf; Clemen, Christoph S