Dissecting the effect of mitochondrial BCAT inhibition in methylmalonic acidemia.
剖析线粒体 BCAT 抑制对甲基丙二酸血症的影响。
期刊:JCI Insight
影响因子:6.1
doi:10.1172/jci.insight.187758
Hemmingsen Madeline G, Zhang Guo-Fang, Ma Yunhan, Marchuk Hannah, Patel Kalyani R, Chen Tong, Li Xinning, Chapman Mark, Collias Sabrina, Lopez-Terrada Dolores H, Beasley James, Stiles Ashlee R, Chandler Randy J, Venditti Charles P, Young Sarah P, Barzi Mercedes, Bissig-Choisat Beatrice, Krafte Doug, Newgard Christopher B, Bissig Karl-Dimiter