日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Somatic deficiency of the human E3 ubiquitin ligase CBL in leukocytes impairs B cell but not T cell development and function.

白细胞中人类 E3 泛素连接酶 CBL 的体细胞缺陷会损害 B 细胞的发育和功能,但不会影响 T 细胞的发育和功能。

Vatovec Taja, Neehus Anna-Lena, Jackson Katherine J L, Avery Danielle T, Bagarić Ivan, Erazo Lucia, Arango-Franco Carlos A, Ogishi Masato, Ahmed Syed F, Cederholm Axel, Russell Amanda J, Della Mina Erika, Al-Rifai Dena, Bull Rowena, Buetow Lori, Sobrino Steicy, Zhang Allison, Wahlster Lara, Michelet Marine, Parvaneh Nima, Peel Jessica, Barzaghi Federica, Leardini Davide, Philippot Quentin, Saettini Francesco, Dutrieux Jacques, de Muylder Benedicte, Vendemini Francesca, Baccelli Francesco, Catala Albert, Gambineri Eleonora, Veltroni Marinella, Pandiarajan Vignesh, Aguilar Yurena, Haerynck Filomeen, Elliott Michael, Turville Stuart, Brillot Fabienne, Khan Taushif, Consonni Filippo, Berteloot Laureline, Sewell William A, Rao Geetha, Largeaud Laetitia, Conti Francesca, Roullion Cecile, Masson Cécile, Pegoraro Francesco, Ye Tianyi, Joubran Samantha, Villalpando Emily, Bessot Boris, Seeleuthner Yoann, Le Voyer Tom, Rosain Jérémie, Li Hailun, Janda Zarah, Muratore Edoardo, Soudée Camille, Delabesse Eric, Goulvestre Claire, Shahrooei Mohammad, Puel Anne, André Isabelle, Bole-Feysot Christine, Abel Laurent, Erlacher Miriam, Béziat Vivien, Lagresle-Peyrou Chantal, Cheynier Remi, Six Emmanuelle, Marr Nico, Pasquet Marlène, Alsina Laia, Goodnow Christopher C, Landegren Nils, Aiuti Alessandro, Zhang Peng, Masetti Riccardo, Huang Danny T, Ma Cindy S, Casanova Jean-Laurent, Sankaran Vijay G, Bustamante Jacinta, Tangye Stuart G, Bohlen Jonathan

Humanized In Vivo Bone Tissue Engineering: In Vitro Preculture Conditions Control the Structural, Cellular, and Matrix Composition of Humanized Bone Organs

人源化体内骨组织工程:体外预培养条件控制人源化骨器官的结构、细胞和基质组成

Agathe Bessot,Flavia Medeiros Savi,Jennifer Gunter,Jayanti Mendhi,Shahrouz Amini,David Waugh,Jacqui McGovern,Dietmar W Hutmacher,Nathalie Bock

Sponge Morphology of Osteosarcoma Finds Origin in Synergy Between Bone Synthesis and Tumor Growth

骨肉瘤的海绵状形态源于骨合成与肿瘤生长之间的协同作用

Bardouil, Arnaud; Bizien, Thomas; Amiaud, Jérome; Fautrel, Alain; Battaglia, Séverine; Almarouk, Iman; Rouxel, Tanguy; Panizza, Pascal; Perez, Javier; Last, Arndt; Djediat, Chakib; Bessot, Elora; Nassif, Nadine; Rédini, Françoise; Artzner, Franck

FLT3L governs the development of partially overlapping hematopoietic lineages in humans and mice

FLT3L 调控人类和小鼠中部分重叠的造血谱系的发育

Mana Momenilandi,Romain Lévy,Steicy Sobrino,Jingwei Li,Chantal Lagresle-Peyrou,Hossein Esmaeilzadeh,Antoine Fayand,Corentin Le Floc'h,Antoine Guérin,Erika Della Mina,Debra Shearer,Ottavia M Delmonte,Ahmad Yatim,Kevin Mulder,Mathieu Mancini,Darawan Rinchai,Adeline Denis,Anna-Lena Neehus,Karla Balogh,Sarah Brendle,Hassan Rokni-Zadeh,Majid Changi-Ashtiani,Yoann Seeleuthner,Caroline Deswarte,Boris Bessot,Cassandre Cremades,Marie Materna,Axel Cederholm,Masato Ogishi,Quentin Philippot,Omer Beganovic,Mania Ackermann,Margareta Wuyts,Taushif Khan,Sébastien Fouéré,Florian Herms,Johan Chanal,Boaz Palterer,Julie Bruneau,Thierry J Molina,Stéphanie Leclerc-Mercier,Jean-Luc Prétet,Leila Youssefian,Hassan Vahidnezhad,Nima Parvaneh,Kristl G Claeys,Rik Schrijvers,Marine Luka,Philippe Pérot,Jacques Fourgeaud,Céline Nourrisson,Philippe Poirier,Emmanuelle Jouanguy,Stéphanie Boisson-Dupuis,Jacinta Bustamante,Luigi D Notarangelo,Neil Christensen,Nils Landegren,Laurent Abel,Nico Marr,Emmanuelle Six,David Langlais,Tim Waterboer,Florent Ginhoux,Cindy S Ma,Stuart G Tangye,Isabelle Meyts,Nico Lachmann,Jiafen Hu,Mohammad Shahrooei,Xavier Bossuyt,Jean-Laurent Casanova,Vivien Béziat

Autoinflammation in patients with leukocytic CBL loss of heterozygosity is caused by constitutive ERK-mediated monocyte activation

白细胞性CBL杂合性缺失患者的自身炎症是由组成型ERK介导的单核细胞活化引起的。

Bohlen, Jonathan; Bagarić, Ivan; Vatovec, Taja; Ogishi, Masato; Ahmed, Syed F; Cederholm, Axel; Buetow, Lori; Sobrino, Steicy; Le Floc'h, Corentin; Arango-Franco, Carlos A; Seabra, Luis; Michelet, Marine; Barzaghi, Federica; Leardini, Davide; Saettini, Francesco; Vendemini, Francesca; Baccelli, Francesco; Catala, Albert; Gambineri, Eleonora; Veltroni, Marinella; Aguilar de la Red, Yurena; Rice, Gillian I; Consonni, Filippo; Berteloot, Laureline; Largeaud, Laetitia; Conti, Francesca; Roullion, Cécile; Masson, Cécile; Bessot, Boris; Seeleuthner, Yoann; Le Voyer, Tom; Rinchai, Darawan; Rosain, Jérémie; Neehus, Anna-Lena; Erazo-Borrás, Lucia; Li, Hailun; Janda, Zarah; Cho, En-Jui; Muratore, Edoardo; Soudée, Camille; Lainé, Candice; Delabesse, Eric; Goulvestre, Claire; Ma, Cindy S; Puel, Anne; Tangye, Stuart G; André, Isabelle; Bole-Feysot, Christine; Abel, Laurent; Erlacher, Miriam; Zhang, Shen-Ying; Béziat, Vivien; Lagresle-Peyrou, Chantal; Six, Emmanuelle; Pasquet, Marlène; Alsina, Laia; Aiuti, Alessandro; Zhang, Peng; Crow, Yanick J; Landegren, Nils; Masetti, Riccardo; Huang, Danny T; Casanova, Jean-Laurent; Bustamante, Jacinta

RAC2 gain-of-function variants causing inborn error of immunity drive NLRP3 inflammasome activation

RAC2功能获得性变异导致先天性免疫缺陷,进而激活NLRP3炎症小体。

Anne Doye #,Paul Chaintreuil #,Chantal Lagresle-Peyrou #,Ludovic Batistic,Valentine Marion,Patrick Munro,Celine Loubatier,Rayana Chirara,Nataël Sorel,Boris Bessot,Pauline Bronnec,Julie Contenti,Johan Courjon,Valerie Giordanengo,Arnaud Jacquel,Pascal Barbry,Marie Couralet,Nathalie Aladjidi,Alain Fischer,Marina Cavazzana,Coralie Mallebranche,Orane Visvikis,Sven Kracker,Despina Moshous,Els Verhoeyen,Laurent Boyer

ECM-mimicking hydrogel models of human adipose tissue identify deregulated lipid metabolism in the prostate cancer-adipocyte crosstalk under antiandrogen therapy

模拟 ECM 的人体脂肪组织水凝胶模型可识别抗雄激素治疗下前列腺癌-脂肪细胞串扰中失调的脂质代谢

Agathe Bessot, Joan Röhl, Maria Emmerich, Anton Klotz, Akhilandeshwari Ravichandran, Christoph Meinert, David Waugh, Jacqui McGovern, Jenni Gunter, Nathalie Bock2

Restoration of T and B Cell Differentiation after RAG1 Gene Transfer in Human RAG1 Defective Hematopoietic Stem Cells

RAG1 基因转移至人类 RAG1 缺陷造血干细胞后 T 细胞和 B 细胞分化的恢复

Nataël Sorel, Francisco Díaz-Pascual, Boris Bessot, Hanem Sadek, Chloé Mollet, Myriam Chouteau, Marco Zahn, Irene Gil-Farina, Parisa Tajer, Marja van Eggermond, Dagmar Berghuis, Arjan C Lankester, Isabelle André, Richard Gabriel, Marina Cavazzana, Kasrin Pike-Overzet, Frank J T Staal, Chantal Lagres

Effects of acute bouts of evening resistance or endurance exercises on sleep EEG and salivary cortisol

傍晚进行急性阻力或耐力训练对睡眠脑电图和唾液皮质醇的影响

Perrier, Joy; Langeard, Antoine; Ouma, Chandrou Koumar; Sesboüé, Bruno; Clochon, Patrice; Prevost, Jean-Noël; Bertran, Françoise; Davenne, Damien; Bessot, Nicolas

Effectiveness of multi-modal home-based videoconference interventions on sleep in older adults: study protocol for a randomized controlled trial

多模式居家视频会议干预对老年人睡眠的影响:一项随机对照试验的研究方案

Milot, Emma; Rehel, Stéphane; Langeard, Antoine; Bigot, Lucile; Pasquier, Florane; Matveeff, Laura; Gauthier, Antoine; Bessot, Nicolas; Quarck, Gaëlle